{"id":1964,"date":"2012-02-04T18:57:04","date_gmt":"2012-02-04T15:57:04","guid":{"rendered":"http:\/\/www.werathah.com\/meta\/?p=1964"},"modified":"2025-11-15T13:00:55","modified_gmt":"2025-11-15T10:00:55","slug":"mucopolysaccharidosis","status":"publish","type":"post","link":"https:\/\/www.werathah.com\/meta\/metabolic\/mucopolysaccharidosis\/","title":{"rendered":"\u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631\u064a\u0627\u062a \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629"},"content":{"rendered":"<p><strong>\u0623\u0645\u0631\u0627\u0636 \u0639\u062f\u064a\u062f\u0627\u062a <\/strong><\/p>\n<p><strong>\u0627\u0644\u0633\u0643\u0631\u064a\u0627\u062a \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629<\/strong><\/p>\n<p>Mucopolysaccharidosis<\/p>\n<p>&nbsp;<\/p>\n<p>\u0647\u064a \u0623\u0645\u0631\u0627\u0636 \u0648\u0631\u0627\u062b\u064a\u0629 \u0646\u0627\u062c\u0645\u0629 \u0639\u0646 \u062e\u0644\u0644 \u0641\u064a \u0645\u0627 \u064a\u0633\u0645\u0649 \u0627\u0644\u0644\u064a\u0633\u0648\u0633\u0648\u0645 (lysosome) \u0648\u0647\u0648 \u0627\u0644\u062c\u0632\u0621 \u0627\u0644\u0645\u0633\u0626\u0648\u0644 \u0639\u0646 \u062d\u0631\u0642 recycling) ( \u0627\u0644\u0645\u0648\u0627\u062f \u063a\u064a\u0631 \u0627\u0644\u0645\u0631\u063a\u0648\u0628 \u0641\u064a\u0647\u0627 \u062f\u0627\u062e\u0644 \u0627\u0644\u062e\u0644\u0627\u064a\u0627 \u0648\u062a\u0633\u0645\u0649 \u0623\u0645\u0631\u0627\u0636 \u062a\u062e\u0632\u064a\u0646 ( Storage Disease)\u00a0 \u0644\u0623\u0646 \u0627\u0644\u062c\u0633\u0645 \u064a\u0638\u0644 \u0639\u0627\u062c\u0632\u0627 \u0639\u0646 \u0643\u0646\u0633 \u0648\u062d\u0631\u0642 \u0648\u062a\u0643\u0633\u064a\u0631 \u062a\u0644\u0643 \u0627\u0644\u0645\u0648\u0627\u062f.<\/p>\n<p>\u0623\u0645\u0627 \u0643\u064a\u0641\u00a0 \u0644\u0627 \u062a\u0633\u062a\u0637\u064a\u0639 \u0627\u0644\u062e\u0644\u064a\u0629 \u0627\u0644\u062a\u062e\u0644\u0635 \u0645\u0646 \u0645\u0648\u0627\u062f \u0645\u062e\u0632\u0646\u0629 \u0639\u0644\u064a\u0647\u0627 \u060c \u0641\u0647\u0630\u0627 \u0646\u0627\u062a\u062c \u0639\u0646 \u0639\u062f\u0645 \u0642\u062f\u0631\u062a\u0647\u0627 \u0639\u0644\u0649 \u0625\u0646\u062a\u0627\u062c \u0627\u0644\u0625\u0646\u0632\u064a\u0645 \u0627\u0644\u0645\u0633\u0626\u0648\u0644 \u0639\u0646 \u062a\u0643\u0633\u064a\u0631 \u062a\u0644\u0643 \u0627\u0644\u0645\u0648\u0627\u062f \u0648\u0647\u064a \u0639\u0645\u0644\u064a\u0629 \u0645\u0633\u0626\u0648\u0644 \u0639\u0646\u0647\u0627 \u0627\u0644\u0644\u0633\u064a\u0633\u0648\u0645 \u0639\u0628\u0631 \u0627\u0644\u0623\u0646\u0632\u064a\u0645\u0627\u062a \u0627\u0644\u062a\u064a \u064a\u0646\u062a\u062c\u0647\u0627\u00a0 ( Lysosomal Enzymes )<\/p>\n<p>\u0639\u0627\u062f\u0629\u00a0 \u0627\u0644\u062c\u0633\u0645\u00a0 \u064a\u0633\u062a\u062e\u062f\u0645 \u0627\u0644\u0625\u0646\u0632\u064a\u0645\u0627\u062a \u0644\u062d\u0631\u0642 \u0648\u0625\u0632\u0627\u0644\u0629 \u0627\u0644\u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u0645\u064a\u062a\u0629\u00a0 \u0643\u062c\u0632\u0621 \u0645\u0646 \u0639\u0645\u0644\u064a\u0629 \u0627\u0644\u0628\u0646\u0627\u0621 \u0648\u0627\u0644\u0647\u062f\u0645 \u0627\u0644\u0645\u0633\u062a\u0645\u0631\u0629 \u0641\u064a \u062c\u0633\u0645 \u0627\u0644\u0625\u0646\u0633\u0627\u0646. \u0644\u0643\u0646 \u0641\u064a \u0647\u0630\u0627 \u0627\u0644\u0646\u0648\u0639 \u0645\u0646 \u0627\u0644\u0623\u0645\u0631\u0627\u0636 \u0644\u0627 \u064a\u0645\u0644\u0643 \u0627\u0644\u0645\u0631\u064a\u0636 \u0627\u0644\u0625\u0646\u0632\u064a\u0645 \u0627\u0644\u0645\u062d\u062f\u062f \u0644\u0641\u0639\u0644 \u0630\u0644\u0643 \u0623\u0648 \u0623\u0646 \u0627\u0644\u0625\u0646\u0632\u064a\u0645 \u064a\u0648\u062c\u062f \u0628\u0635\u0648\u0631\u0629 \u0642\u0644\u064a\u0644\u0629 \u0648\u063a\u064a\u0631 \u0643\u0627\u0641\u064a\u0629. \u0628\u062d\u064a\u062b \u0644\u0627 \u064a\u0639\u0648\u062f \u0645\u0645\u0643\u0646\u0627 \u0627\u0644\u062d\u0631\u0642 \u0648\u0627\u0644\u062a\u0643\u0633\u064a\u0631 \u0648\u0628\u0627\u0644\u062a\u0627\u0644\u064a \u0644\u0627 \u064a\u0645\u0643\u0646 \u0627\u0644\u062a\u062e\u0644\u0635 \u0645\u0646 \u0627\u0644\u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u0645\u064a\u062a\u0629. \u0648\u0627\u0644\u0646\u062a\u064a\u062c\u0629\u00a0 \u062a\u0631\u0627\u0643\u0645 \u0627\u0644\u0645\u0648\u0627\u062f \u0627\u0644\u0645\u064a\u062a\u0629 \u0641\u064a \u0643\u0644 \u062e\u0644\u064a\u0629 \u0645\u0646 \u0627\u0644\u062c\u0633\u0645 \u062a\u0642\u0631\u064a\u0628\u0627 \u0648\u062a\u0643\u0648\u0646 \u0628\u0630\u0644\u0643 \u0627\u0644\u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u0645\u064a\u062a\u0629 \u0639\u0628\u0626\u0627 \u0639\u0644\u0649 \u0627\u0644\u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u062d\u064a\u0629 \u0641\u0644\u0627 \u062a\u0633\u062a\u0637\u064a\u0639 \u0627\u0644\u0623\u062e\u064a\u0631\u0629 \u0627\u0644\u0642\u064a\u0627\u0645 \u0628\u0645\u0647\u0627\u0645\u0647\u0627 \u0628\u0635\u0648\u0631\u0629 \u0639\u0627\u062f\u064a\u0629. \u0648\u0628\u0647\u0630\u0627 \u064a\u062d\u062f\u062b \u062f\u0645\u0627\u0631 \u0645\u062a\u0632\u0627\u064a\u062f \u0648\u0645\u062a\u0637\u0648\u0631 \u0641\u064a \u0643\u0644 \u0623\u062c\u0632\u0627\u0621 \u0627\u0644\u062c\u0633\u0645 \u0628\u0645\u0627 \u0641\u064a \u0630\u0644\u0643 \u0627\u0644\u0642\u0644\u0628 \u0648\u0627\u0644\u0639\u0638\u0627\u0645 \u0648\u0627\u0644\u0645\u0641\u0627\u0635\u0644 \u0648\u0627\u0644\u062c\u0647\u0627\u0632 \u0627\u0644\u062a\u0646\u0641\u0633\u064a \u0648\u0627\u0644\u062c\u0647\u0627\u0632 \u0627\u0644\u0639\u0635\u0628\u064a.<\/p>\n<p>\u0647\u0630\u0647 \u0627\u0644\u0623\u0645\u0631\u0627\u0636 \u0631\u063a\u0645 \u0623\u0646\u0647\u0627 \u0644\u0627 \u062a\u0643\u0648\u0646 \u0648\u0627\u0636\u062d\u0629 \u0639\u0646\u062f \u0648\u0644\u0627\u062f\u0629 \u0627\u0644\u0637\u0641\u0644 \u0625 \u0644\u0627 \u0623\u0646 \u0639\u0644\u0627\u0645\u0627\u062a\u0647\u0627 \u062a\u0628\u062f\u0623 \u0641\u064a \u0627\u0644\u0638\u0647\u0648\u0631 \u062a\u062f\u0631\u064a\u062c\u064a\u0627 \u0645\u0639 \u062a\u0637\u0648\u0631 \u0627\u0644\u0645\u0631\u0636 \u0627\u0644\u0630\u064a \u064a\u062a\u0637\u0648\u0631 \u0645\u0639 \u0632\u064a\u0627\u062f\u0629 \u0639\u0645\u0631 \u0627\u0644\u0637\u0641\u0644 \u062d\u064a\u062b \u064a\u062a\u0645 \u0625\u062d\u062f\u0627\u062b \u0627\u0644\u0645\u0632\u064a\u062f \u0645\u0646 \u0627\u0644\u0636\u0631\u0631 \u0644\u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u062c\u0633\u0645 \u0644\u0623\u0646 \u0627\u0644\u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u0645\u064a\u062a\u0629 \u062a\u062a\u0631\u0627\u0643\u0645 \u0639\u0644\u064a\u0647\u0627 \u0628\u0645\u0631\u0648\u0631 \u0627\u0644\u0623\u064a\u0627\u0645.<\/p>\n<p>\u0623\u0645\u0631\u0627\u0636 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631\u064a\u0627\u062a \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629 \u0623\u0648 \u0639\u062f\u064a\u062f \u0627\u0644\u0633\u0643\u0631\u064a\u0627\u062a \u0627\u0644\u0645\u062e\u0627\u0637\u064a (mucopolysaccharidosis) \u062a\u0635\u064a\u0628 \u0648\u0627\u062d\u062f\u0627 \u0645\u0646 \u0628\u064a\u0646 \u0643\u0644 \u062e\u0645\u0633\u0629 \u0648\u0639\u0634\u0631\u064a\u0646 \u0623\u0644\u0641 \u0645\u0648\u0644\u0648\u062f \u062a\u0642\u0631\u064a\u0628\u0627. \u0648\u0647\u064a \u0623\u0645\u0631\u0627\u0636 \u062a\u0633\u0628\u0628 \u0625\u0639\u0627\u0642\u0629 \u062c\u0633\u062f\u064a\u0629 \u0645\u062a\u0637\u0648\u0631\u0629 \u0648\u0645\u0633\u062a\u0645\u0631\u0629 \u0648\u0641\u064a \u0627\u0644\u0639\u062f\u064a\u062f \u0645\u0646 \u0627\u0644\u062d\u0627\u0644\u0627\u062a \u062a\u0648\u062c\u062f \u0625\u0639\u0627\u0642\u0629 \u0639\u0642\u0644\u064a\u0629 \u0634\u062f\u064a\u062f\u0629 \u0648\u0639\u0627\u062f\u0629 \u064a\u0645\u0648\u062a \u0627\u0644\u0645\u0635\u0627\u0628\u0648\u0646 \u0648\u0647\u0645 \u0641\u064a \u0639\u0645\u0631 \u0627\u0644\u0637\u0641\u0648\u0644\u0629 \u0644\u0643\u0646 \u0647\u0646\u0627\u0643 \u0627\u0633\u062a\u062b\u0646\u0627\u0621\u0627\u062a \u064a\u0637\u0648\u0644 \u0641\u064a\u0647\u0627 \u0627\u0644\u0639\u0645\u0631.<\/p>\n<p><strong> \u0623\u0642\u0633\u0627\u0645 \u0645\u0631\u0636 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631 \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629 <\/strong><\/p>\n<p>\u064a\u0646\u0642\u0633\u0645 \u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 \u0625\u0644\u0649 \u0633\u0628\u0639\u0629 \u0623\u0642\u0633\u0627\u0645 \u0648\u064a\u0633\u0645\u0649 \u0643\u0644 \u0646\u0648\u0639 \u0628\u0627\u0633\u0645 \u0627\u0644\u0637\u0628\u064a\u0628 \u0627\u0644\u0630\u064a \u0627\u0643\u062a\u0634\u0641\u0647.<\/p>\n<p>\u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0623\u0648\u0644\u00a0\u00a0 MPS-1\u0623\u0648 MPS IHS<\/p>\n<p>\u0648\u0647\u0630\u0627 \u0627\u0644\u0646\u0648\u0639 \u064a\u0646\u0642\u0633\u0645 \u0625\u0644\u0649 \u062b\u0644\u0627\u062b\u0629 \u0623\u0642\u0633\u0627\u0645<\/p>\n<p>(\u0623\u200c)\u0645\u062a\u0644\u0627\u0632\u0645\u0629\u00a0 \u0647\u064a\u0631\u0644\u0648\u0631\u00a0\u00a0\u00a0 (\u0625\u0635\u0627\u0628\u0629 \u0634\u062f\u064a\u062f\u0629)<\/p>\n<p>(\u0628\u200c)\u0645\u062a\u0644\u0627\u0632\u0645\u0629\u00a0 \u0647\u064a\u0631\u0644\u0631 \u0633\u0643\u064a ( \u0625\u0635\u0627\u0628\u0629 \u0645\u062a\u0648\u0633\u0637\u0629)<\/p>\n<p>(\u0628\u200c)\u0645\u062a\u0644\u0627\u0632\u0645\u0629\u00a0 \u0633\u0643\u064a (\u0623\u062d\u064a\u0627\u0646\u0627 \u062a\u0643\u062a\u0628 \u062a\u0634\u0627\u064a). (\u0625\u0635\u0627\u0628\u0629 \u062e\u0641\u064a\u0641\u0629)<\/p>\n<p>\u0627\u0644\u062a\u0642\u0633\u064a\u0645\u0627\u062a \u0627\u0644\u062b\u0644\u0627\u062b\u0629 \u0647\u064a \u062a\u0633\u0645\u064a\u0627\u062a \u0644\u0645\u0631\u0636 \u0648\u0627\u062d\u062f ( Mucopolysaccharidosis Type 1 )\u062d\u064a\u062b \u0627\u0644\u0625\u0646\u0632\u064a\u0645 \u0627\u0644\u0645\u0641\u0642\u0648\u062f \u0648\u0627\u062d\u062f \u0643\u0645\u0627 \u0633\u064a\u0623\u062a\u064a \u0634\u0631\u062d \u0630\u0644\u0643.<\/p>\n<p>\u0648\u0642\u062f \u0623\u062e\u0630 \u0627\u0644\u0645\u0631\u0636 \u0627\u0633\u0645\u0647- \u0647\u064a\u0631\u0644\u0648\u0631- \u0645\u0646 \u0627\u0644\u0637\u0628\u064a\u0628 \u062c\u064a\u0631\u062a\u0631\u062f \u0647\u064a\u0631\u0644\u0648\u0631\u00a0\u00a0\u00a0 Gertrud Hurler \u0627\u0644\u0630\u064a \u0648\u0635\u0641 \u0637\u0641\u0644\u0627 \u0648\u0637\u0641\u0644\u0629 \u0628\u0639\u0644\u0627\u0645\u0627\u062a \u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 \u0641\u064a \u0627\u0644\u0639\u0627\u0645 \u0623\u0644\u0641 \u0648\u062a\u0633\u0639\u0645\u0627\u0626\u0629 \u0648\u062a\u0633\u0639\u0629 \u0639\u0634\u0631. \u0648\u0641\u064a \u0639\u0627\u0645\u00a0 \u0623\u0644\u0641 \u0648\u062a\u0633\u0639\u0645\u0627\u0626\u0629 \u0648\u0627\u062b\u0646\u064a\u0646 \u0648\u0633\u062a\u064a\u0646 \u0643\u062a\u0628 \u0627\u0644\u0627\u0633\u062a\u0634\u0627\u0631\u064a \u0641\u064a \u0623\u0645\u0631\u0627\u0636 \u0627\u0644\u0639\u064a\u0648\u0646 \u062f\u0643\u062a\u0648\u0631 \u0633\u0643\u064a\u00a0\u00a0 Schie\u00a0 \u0639\u0646 \u0645\u0631\u0636\u0649 \u0643\u0627\u0646\u062a \u0625\u0635\u0627\u0628\u0627\u062a\u0647\u0645 \u0623\u0642\u0644 \u0636\u0631\u0627\u0648\u0629. \u0623\u0645\u0627 \u0627\u0644\u0645\u0631\u0636\u0649 \u0627\u0644\u0630\u064a\u0646 \u0644\u0627 \u064a\u0648\u0635\u0641\u0648\u0646 \u0628\u0623\u0646 \u0625\u0635\u0627\u0628\u062a\u0647\u0645 \u0634\u062f\u064a\u062f\u0629 \u0623\u0648 \u062e\u0641\u064a\u0641\u0629 \u0641\u0625\u0646\u0647\u0645 \u064a\u0639\u0631\u0641\u0648\u0646 \u0628\u062f\u0645\u062c \u0627\u0644\u0627\u0633\u0645\u064a\u0646 \u0645\u0639\u0627 \u0647\u064a\u0631\u0644\u0648\u0631- \u0633\u0643\u064a Hurler\/Schie\u00a0 .<\/p>\n<p><a href=\"https:\/\/www.werathah.com\/meta\/mucopoly2.htm\">\u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u062b\u0627\u0646\u064a MPS-2<\/a><\/p>\n<p>\u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u062b\u0627\u0644\u062b MPS-3<\/p>\n<p>\u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0631\u0627\u0628\u0639 MPS-4<\/p>\n<p>\u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u062e\u0627\u0645\u0633\u00a0 MPS-5<\/p>\n<p>\u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0633\u0627\u062f\u0633 MPS-6<\/p>\n<p>\u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0633\u0627\u0628\u0639\u00a0 MPS-7<\/p>\n<p><strong><br \/>\n\u0637\u0628\u064a\u0639\u0629 \u0627\u0644\u0645\u0631\u0636 \u0648\u0623\u0633\u0628\u0627\u0628\u0647<\/strong><\/p>\n<p>mucopolysaccharidosis \u0647\u064a \u0633\u0644\u0633\u0644\u0629 \u0637\u0648\u064a\u0644\u0629 \u0645\u0646 \u062c\u0632\u064a\u0621 \u0627\u0644\u0633\u0643\u0631 \u062a\u0633\u062a\u062e\u062f\u0645 \u0641\u064a \u0628\u0646\u0627\u0621\u00a0\u00a0\u00a0\u00a0\u00a0\u00a0 \u0627\u0644\u0646\u0633\u064a\u062c \u0627\u0644\u0636\u0627\u0645 Connective tissue<\/p>\n<p>saccharide \u0647\u0648 \u0627\u0635\u0637\u0644\u0627\u062d \u0639\u0627\u0645 \u064a\u0637\u0644\u0642 \u0639\u0644\u0649 \u062c\u0632\u064a\u0621 \u0627\u0644\u0633\u0643\u0631<\/p>\n<p>Poly \u062a\u0639\u0646\u064a \u0645\u062a\u0639\u062f\u062f \u0623\u0648 \u0639\u062f\u064a\u062f\u0627\u062a.<\/p>\n<p>\u0648\u0628\u0647\u0630\u0627 \u064a\u062c\u064a\u0621 \u0627\u0644\u0627\u0633\u0645 \u0645\u0646 \u0627\u0644\u0643\u0644\u0645\u0627\u062a \u0627\u0644\u062b\u0644\u0627\u062b mucopolysaccharidosis .<\/p>\n<p>\u0647\u0646\u0627\u0643 \u0639\u0645\u0644\u064a\u0629 \u0645\u0633\u062a\u0645\u0631\u0629 \u0641\u064a \u0627\u0644\u062c\u0633\u0645 \u0644\u062a\u063a\u064a\u064a\u0631 \u0627\u0644\u0645\u0648\u0627\u062f \u0627\u0644\u062a\u064a \u062a\u0645 \u0627\u0633\u062a\u062e\u062f\u0627\u0645\u0647\u0627 \u0648\u062d\u0631\u0642\u0647\u0627 \u0628\u063a\u0631\u0636 \u0627\u0644\u062a\u062e\u0644\u0635 \u0645\u0646\u0647\u0627. \u0627\u0644\u0623\u0637\u0641\u0627\u0644 \u0627\u0644\u0645\u0635\u0627\u0628\u0648\u0646 \u0628\u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 mps1\u00a0 \u064a\u0646\u0642\u0635\u0647\u0645 \u0625\u0646\u0632\u064a\u0645 \u064a\u0633\u0645\u0649\u00a0\u00a0 Alpha-L-Iduronidase\u00a0 \u0648\u0647\u0648 \u0627\u0644\u0625\u0646\u0632\u064a\u0645 \u0627\u0644\u0645\u0633\u0626\u0648\u0644 \u0639\u0646 \u062d\u0631\u0642 \u062c\u0632\u064a\u0626\u0627\u062a \u0627\u0644\u0633\u0643\u0631 \u0627\u0644\u0645\u0633\u0645\u0627\u0629 dermatan sulfate and heparan sulfate glycosaminoglycans \u0648\u0647\u064a \u062a\u062e\u062a\u0635\u0631 \u0639\u0645\u0648\u0645\u0627 \u0628\u0627\u0633\u0645\u00a0 GAGs.\u0648\u0647\u0630\u0647 \u0627\u0644\u062c\u0632\u064a\u0626\u0627\u062a \u0627\u0644\u062a\u064a \u0644\u0627 \u064a\u062a\u0645 \u062d\u0631\u0642\u0647\u0627 \u0648\u062a\u0643\u0633\u064a\u0631\u0647\u0627 \u0628\u0635\u0648\u0631\u0629 \u0643\u0627\u0645\u0644\u0629 \u062a\u0628\u0642\u0649 \u0645\u062e\u0632\u0646\u0629 \u0641\u064a \u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u062c\u0633\u0645 \u0645\u0633\u0628\u0628\u0629 \u062f\u0645\u0627\u0631\u0627 \u0645\u0633\u062a\u0645\u0631\u0627 \u0648\u0645\u062a\u0635\u0627\u0639\u062f\u0627 \u0648\u0645\u062a\u0633\u0639 \u0627\u0644\u0646\u0637\u0627\u0642.\u00a0 \u0627\u0644\u0623\u0637\u0641\u0627\u0644 \u062d\u062f\u064a\u062b\u0648 \u0627\u0644\u0648\u0644\u0627\u062f\u0629 \u064a\u0645\u0643\u0646 \u0623\u0646 \u062a\u0638\u0647\u0631 \u0639\u0644\u064a\u0647\u0645 \u0639\u0644\u0627\u0645\u0627\u062a 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\u0639\u062f\u0627 \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u062b\u0627\u0646\u064a Hunter syndrome \u0648\u0633\u064a\u0623\u062a\u064a \u0627\u0644\u062d\u062f\u064a\u062b \u0639\u0646\u0647 \u0644\u0627\u062d\u0642\u0627. \u0643\u0644 \u0645\u0646\u0627 \u0644\u0647 \u0645\u0648\u0631\u062b\u0627\u062a\u00a0 Genes \u0648\u0631\u062b\u0647\u0627 \u0645\u0646 \u0648\u0627\u0644\u062f\u064a\u0647 . \u0648\u0647\u0630\u0647 \u0627\u0644\u0645\u0648\u0631\u062b\u0627\u062a \u062a\u062d\u062f\u062f \u0627\u0644\u0635\u0641\u0627\u062a \u0627\u0644\u0648\u0631\u0627\u062b\u064a\u0629 \u0645\u062b\u0644 \u0627\u0644\u0637\u0648\u0644 \u0648\u0627\u0644\u0642\u0635\u0631 \u0648\u0627\u0644\u0644\u0648\u0646 \u0648\u063a\u064a\u0631\u0647\u0627. \u0628\u0639\u0636 \u0627\u0644\u062c\u064a\u0646\u0627\u062a \u0627\u0644\u062a\u064a \u0646\u0631\u062b\u0647\u0627 \u062a\u0643\u0648\u0646 \u0645\u062a\u0646\u062d\u064a\u0629 \u0648\u0647\u0648 \u0645\u0627 \u064a\u0641\u0633\u0631 \u0639\u0628\u0627\u0631\u0629 \u0623\u0646\u0646\u0627 \u0646\u062d\u0645\u0644 \u0630\u0644\u0643 \u0627\u0644\u062c\u064a\u0646 \u0648\u0644\u0643\u0646\u0647 \u0644\u0627 \u064a\u0624\u062b\u0631 \u0639\u0644\u0649 \u0635\u062d\u062a\u0646\u0627\u00a0 \u0631\u063a\u0645 \u0623\u0646\u0647 \u062c\u064a\u0646 \u0645\u0639\u0637\u0648\u0628.Hurler disease\u00a0\u00a0\u00a0\u00a0 \u0623\u0648\u00a0 \u0647\u064a\u0631\u0644\u0648\u0631 \u0633\u064a\u0646\u062f\u0631\u0648\u0645\u00a0 Hurler Syndrome\u00a0 ( \u0645\u062a\u0644\u0627\u0632\u0645\u0629 \u0647\u064a\u0631\u0644\u0648\u0631) \u064a\u0633\u0628\u0628\u0647\u0627\u00a0 \u0645\u0648\u0631\u062b \u0645\u062a\u0646\u062d Recessive gene . \u0641\u0625\u0630\u0627 \u062a\u0632\u0648\u062c \u0634\u062e\u0635 \u064a\u062d\u0645\u0644 \u0627\u0644\u062c\u064a\u0646 \u0627\u0644\u0645\u0639\u0637\u0648\u0628 \u0645\u0646 \u0622\u062e\u0631 \u064a\u062d\u0645\u0644 \u0630\u0627\u062a \u0627\u0644\u062c\u064a\u0646 \u0641\u0625\u0646 \u0647\u0646\u0627\u0643 \u0627\u062d\u062a\u0645\u0627\u0644\u0627 \u0646\u0633\u0628\u062a\u0647 \u062e\u0645\u0633\u0629 \u0648\u0639\u0634\u0631\u0648\u0646 \u0628\u0627\u0644\u0645\u0626\u0629 \u0628\u0623\u0646 \u064a\u0635\u0627\u0628 \u0627\u0644\u0645\u0648\u0644\u0648\u062f \u0628\u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636. \u0648\u0647\u0630\u0627 \u0627\u0644\u0627\u062d\u062a\u0645\u0627\u0644 \u064a\u062a\u062c\u062f\u062f \u0641\u064a \u0643\u0644 \u062d\u0627\u0644\u0629 \u062d\u0645\u0644 \u0623\u064a \u0644\u064a\u0633 \u0644\u0647 \u0639\u0644\u0627\u0642\u0629 \u0628\u0627\u0644\u0648\u0644\u0627\u062f\u0627\u062a \u0627\u0644\u0633\u0627\u0628\u0642\u0629 \u0623\u0648 \u0627\u0644\u0644\u0627\u062d\u0642\u0629 . \u0648\u0647\u0646\u0627\u0643 \u0627\u062d\u062a\u0645\u0627\u0644 \u0628\u0646\u0633\u0628\u0629 \u0627\u062b\u0646\u062a\u064a\u0646 \u0645\u0646 \u0628\u064a\u0646 \u0643\u0644 \u062b\u0644\u0627\u062b \u0641\u0631\u0635 \u0628\u0623\u0646 \u064a\u0643\u0648\u0646 \u0625\u062e\u0648\u0629 \u0627\u0644\u0645\u0648\u0644\u0648\u062f \u0627\u0644\u0645\u0635\u0627\u0628 \u062d\u0627\u0645\u0644\u064a\u0646 \u0644\u0644\u0645\u0631\u0636 carriers\u00a0\u00a0 \u0648\u0644\u064a\u0633\u0648\u0627 \u0645\u0635\u0627\u0628\u064a\u0646 .<\/p>\n<p>\u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 mucopolysaccharidosis\u00a0 \u0646\u0627\u062f\u0631 \u062c\u062f\u0627 \u0648\u0627\u062d\u062a\u0645\u0627\u0644\u00a0 \u0623\u0646\u00a0 \u064a\u062a\u0632\u0648\u062c \u0634\u062e\u0635 \u062d\u0627\u0645\u0644 \u0645\u0646 \u0622\u062e\u0631 \u062d\u0627\u0645\u0644 \u0623\u064a\u0636\u0627 \u064a\u0639\u062f \u0627\u062d\u062a\u0645\u0627\u0644\u0627 \u0636\u0626\u064a\u0644\u0627 \u062c\u062f\u0627 \u0648\u064a\u0646\u0635\u062d \u0628\u0623\u0646 \u0644\u0627 \u064a\u062a\u0645 \u0632\u0648\u0627\u062c \u0628\u064a\u0646 \u0623\u0628\u0646\u0627\u0621 \u0639\u0645\u0648\u0645\u0629 \u0623\u0648 \u062e\u0624\u0648\u0644\u0629 \u0623\u0648 \u062d\u062a\u0649 \u0623\u0642\u0627\u0631\u0628 \u0642\u0631\u064a\u0628\u064a\u0646 \u062f\u0627\u062e\u0644 \u0623\u0633\u0631\u062a\u0647\u0645 \u0627\u0644\u062a\u064a \u0644\u0647\u0627 \u062a\u0623\u0631\u064a\u062e \u0628\u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636.<\/p>\n<p>\u0644\u0627 \u064a\u0634\u062a\u0631\u0637\u00a0 \u0648\u062c\u0648\u062f \u062a\u0627\u0631\u064a\u062e \u0644\u0644\u0645\u0631\u0636 \u0641\u064a \u0627\u0644\u0623\u0633\u0631\u0629 \u0644\u0625\u062b\u0628\u0627\u062a \u0625\u0635\u0627\u0628\u0629 \u0637\u0641\u0644\u0647\u0627.<\/p>\n<p><strong> \u0627\u0639\u0631\u0627\u0636 \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0623\u0648\u0644 \u0644\u0645\u0631\u0636 \u0639\u062f\u064a\u062f \u0627\u0644\u0633\u0643\u0631 \u0627\u0644\u0645\u062e\u0627\u0637\u064a MPS1 disease<\/strong><\/p>\n<p>\u062a\u0623\u062e\u0631 \u0641\u064a \u0646\u0645\u0648 \u0627\u0644\u062c\u0633\u0645 slowed growth\u00a0 \u0631\u063a\u0645 \u0623\u0646 \u0627\u0644\u0646\u0645\u0648 \u064a\u0643\u0648\u0646 \u0641\u064a \u0627\u0644\u0639\u0627\u062f\u0629 \u0637\u0628\u064a\u0639\u064a\u0627 \u0641\u064a \u0627\u0644\u0639\u0627\u0645 \u0627\u0644\u0623\u0648\u0644 \u0645\u0646 \u0639\u0645\u0631 \u0627\u0644\u0637\u0641\u0644.<\/p>\n<p>\u062a\u0623\u062e\u0631 \u0639\u0642\u0644\u064a \u064a\u062a\u0641\u0627\u0642\u0645 \u0645\u0639 \u0627\u0644\u0648\u0642\u062a\u00a0 mental retardation<\/p>\n<p>\u063a\u0631\u0627\u0628\u0629 \u0645\u0644\u0627\u0645\u062d \u0627\u0644\u0648\u062c\u0647 coarse facial features<\/p>\n<p>\u063a\u0645\u0627\u0645\u0629 \u0628\u064a\u0636\u0627\u0621 \u0641\u064a \u0642\u0631\u0646\u064a\u0629 \u0627\u0644\u0639\u064a\u0646 cloudy cornea \u0628\u0633\u0628\u0628 \u062a\u0631\u0627\u0643\u0645\u00a0 \u0627\u0644\u0633\u0643\u0627\u0631\u0627\u064a\u062f\u0633<\/p>\n<p>\u062a\u062f\u0647\u0648\u0631 \u0641\u064a \u0627\u0644\u0633\u0645\u0639 deafness<\/p>\n<p>\u062a\u064a\u0628\u0633 \u0627\u0644\u0645\u0641\u0627\u0635\u0644\u00a0 joint stiffness<\/p>\n<p>\u0645\u0634\u0627\u0643\u0644 \u0641\u064a \u0635\u0645\u0627\u0645\u0627\u062a \u0627\u0644\u0642\u0644\u0628 valve disease<\/p>\n<p>\u062a\u0634\u0648\u0647\u0627\u062a \u0641\u064a \u0627\u0644\u0642\u0641\u0635 \u0627\u0644\u0635\u062f\u0631\u064a chest deformities<\/p>\n<p>\u062a\u0634\u0648\u0647\u0627\u062a \u0641\u064a \u0627\u0644\u0633\u0644\u0633\u0644\u0629 \u0627\u0644\u0641\u0642\u0631\u064a\u0629 Lordosis, kyphosis<\/p>\n<p>\u0623\u0635\u0627\u0628\u0639 \u0627\u0644\u064a\u062f \u0644\u0647\u0627 \u0634\u0643\u0644 \u0645\u062e\u0644\u0628\u064a claw hand<\/p>\n<p>\u062a\u0634\u0648\u0647\u00a0 \u0627\u0644\u0623\u0633\u0646\u0627\u0646 Tooth deformities<\/p>\n<p>\u0642\u0635\u0631 \u0627\u0644\u0642\u0627\u0645\u0629 Short stature<\/p>\n<p>\u0643\u0628\u0631 \u062d\u062c\u0645 \u0627\u0644\u0631\u0623\u0633 Macrocephaly<\/p>\n<p>\u062a\u0636\u062e\u0645 \u0627\u0644\u0643\u0628\u062f \u0648\u0627\u0644\u0637\u062d\u0627\u0644 Hepatosplenomegaly<\/p>\n<p>\u062a\u0634\u0648\u0647 \u0627\u0644\u0642\u0641\u0635 \u0627\u0644\u0635\u062f\u0631\u064a\u00a0\u00a0 Barrel Chest, Pigeon Chest, Funnel Chest<\/p>\n<p>\u0634\u0641\u0627\u0647 \u0645\u0645\u062a\u0644\u0626\u0629 thick lips<\/p>\n<p>\u0641\u062a\u0627\u0642 \u0627\u0644\u0633\u0631\u0629 inguinal &#8211; umbilical hernia<\/p>\n<p>\u062c\u0628\u0647\u0629 \u0646\u0627\u062a\u0626\u0629 frontal bossing<\/p>\n<p>\u0644\u0633\u0627\u0646 \u0636\u062e\u0645 macroglossia<\/p>\n<p>\u0644\u064a\u0633 \u0628\u0627\u0644\u0636\u0631\u0648\u0631\u0629 \u0623\u0646 \u062a\u0646\u0637\u0628\u0642 \u0643\u0644 \u0647\u0630\u0647 \u0627\u0644\u0639\u0644\u0627\u0645\u0627\u062a \u0639\u0644\u0649 \u0627\u0644\u0645\u0631\u064a\u0636 \u0645\u0639 \u0645\u0644\u0627\u062d\u0638\u0629 \u0623\u0646 \u0645\u0639\u0638\u0645\u0647\u0627 \u0645\u0634\u062a\u0631\u0643 \u0628\u064a\u0646 \u0645\u0639\u0638\u0645 \u0623\u0645\u0631\u0627\u0636 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631 \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629<\/p>\n<p><strong>\u0627\u0644\u0627\u062e\u062a\u0628\u0627\u0631\u0627\u062a \u0627\u0644\u0637\u0628\u064a\u0629 \u0641\u064a\u00a0\u00a0 mps1<\/strong><\/p>\n<p>\u0641\u064a \u0627\u0644\u0628\u062f\u0627\u064a\u0629 \u0639\u0627\u062f\u0629 \u064a\u062c\u0631\u0649 \u0641\u062d\u0635 \u0627\u0644\u0628\u0648\u0644 \u0644\u0642\u064a\u0627\u0633 . dermatan sulfate and heparan sulfate glycosaminoglycans\u00a0 \u0648 \u0627\u0644\u0645\u0635\u0637\u0644\u062d \u0627\u0644\u0639\u0627\u0645 \u0627\u062e\u062a\u0635\u0627\u0631\u0627 \u0647\u0648\u00a0 GAGs \u0627\u0644\u0630\u064a \u064a\u0634\u064a\u0631 \u0625\u0644\u0649 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631 \u0641\u064a \u0627\u0644\u0628\u0648\u0644. \u0644\u0643\u0646 \u0641\u062d\u0635 \u0627\u0644\u0628\u0648\u0644 \u0644\u0627 \u064a\u0648\u0636\u062d \u0646\u0648\u0639 \u0627\u0644\u0645\u0631\u0636 \u0645\u0646 \u0628\u064a\u0646 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631 \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629. \u0648\u0644\u062a\u062d\u062f\u064a\u062f \u0627\u0644\u0646\u0648\u0639 \u064a\u062c\u0628 \u0625\u062c\u0631\u0627\u0621 \u0641\u062d\u0635 \u0646\u0634\u0627\u0637 \u0627\u0644\u0625\u0646\u0632\u064a\u0645 \u0641\u064a \u0627\u0644\u062f\u0645 \u0623\u0648 \u0628\u0623\u062e\u0630 \u0639\u064a\u0646\u0629 \u0645\u0646 \u0627\u0644\u062c\u0644\u062f. \u0648\u0627\u0644\u0627\u0646\u0632\u064a\u0645 \u0627\u0644\u0630\u064a \u064a\u062c\u0628 \u0641\u062d\u0635\u0647 \u0641\u064a \u0647\u0630\u0647 \u0627\u0644\u062d\u0627\u0644\u0629 \u064a\u0633\u0645\u0649\u00a0 alpha-L-iduronidase .\u0623\u064a\u0636\u0627 \u064a\u0645\u0643\u0646 \u0623\u062e\u0630 \u0635\u0648\u0631 \u0623\u0634\u0639\u0629\u00a0 \u0644\u0644\u0639\u0645\u0648\u062f \u0627\u0644\u0641\u0642\u0631\u064a \u0648 \u062a\u062e\u0637\u064a\u0637 \u0644\u0644\u0642\u0644\u0628 \u0644\u0645\u0639\u0631\u0641\u0629 \u0648\u0638\u064a\u0641\u0629 \u0627\u0644\u0642\u0644\u0628 \u0648 \u0627\u0644\u0627\u0637\u0645\u0626\u0646\u0627\u0646 \u0639\u0644\u0649 \u0627\u0644\u0635\u0645\u0627\u0645\u0627\u062a .<\/p>\n<p><strong>\u0627\u0644\u0639\u0644\u0627\u062c:<\/strong><\/p>\n<p>1- \u062d\u062f\u064a\u062b\u0627 \u062a\u0645\u0643\u0646\u062a \u0628\u0639\u0636 \u0627\u0644\u0645\u0624\u0633\u0633\u0627\u062a \u0627\u0644\u0637\u0628\u064a\u0629 \u0645\u0646 \u0625\u0646\u062a\u0627\u062c \u0627\u0644\u0625\u0646\u0632\u064a\u0645 \u0627\u0644\u0645\u0641\u0642\u0648\u062f \u0648\u0627\u0644\u0630\u064a \u064a\u0645\u062b\u0644 \u063a\u064a\u0627\u0628\u0647 \u0623\u0635\u0644 \u0627\u0644\u0645\u0634\u0643\u0644\u0629 \u0648\u0647\u0648 \u064a\u062d\u0642\u0646 \u0641\u064a \u0627\u0644\u062f\u0645 \u0628\u0635\u0648\u0631\u0629 \u0645\u0633\u062a\u0645\u0631\u0629\u00a0 Enzyme Replacement .\u0644\u0643\u0646 \u0627\u0644\u062f\u0631\u0627\u0633\u0627\u062a \u0644\u0627 \u062a\u0632\u0627\u0644 \u0645\u0633\u062a\u0645\u0631\u0629 \u0644\u0645\u0639\u0631\u0641\u0629 \u0645\u062f\u0649 \u0641\u0627\u0639\u0644\u064a\u062a\u0647 \u0648\u0622\u062b\u0627\u0631\u0647 \u0627\u0644\u062c\u0627\u0646\u0628\u064a\u0629 \u0639\u0644\u0649 \u0627\u0644\u0645\u062f\u0649 \u0627\u0644\u0637\u0648\u064a\u0644.<\/p>\n<p>2- \u0632\u0631\u0627\u0639\u0629 \u0646\u062e\u0627\u0639 \u0627\u0644\u0639\u0638\u0645 Bone Marrow Transplant\u00a0\u00a0\u00a0 \u0623\u0648 \u0627\u0644\u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u062c\u0630\u0639\u064a\u0629 \u0627\u0644\u0645\u0633\u062a\u062e\u0631\u062c\u0629 \u0645\u0646 \u062f\u0645 \u0627\u0644\u062d\u0628\u0644 \u0627\u0644\u0633\u0631\u064a \u0645\u0646 \u0645\u062a\u0628\u0631\u0639 \u0645\u0637\u0627\u0628\u0642 \u0628\u062f\u0631\u062c\u0629 \u0643\u0628\u064a\u0631\u0629 Umbilical cord blood stem cell transplants\u00a0 \u0647\u0630\u0627 \u0627\u0644\u0639\u0644\u0627\u062c \u0623\u062b\u0628\u062a \u0641\u0627\u0626\u062f\u0629 \u0644\u0644\u0639\u062f\u064a\u062f \u0645\u0646 \u0627\u0644\u062d\u0627\u0644\u0627\u062a \u0641\u0627\u0633\u062a\u0637\u0627\u0639\u0648\u0627 \u0625\u0646\u062a\u0627\u062c \u0627\u0644\u0625\u0646\u0632\u064a\u0645 \u0628\u062e\u0644\u0627\u064a\u0627\u0647\u0645 \u0627\u0644\u062c\u062f\u064a\u062f\u0629 \u0648\u0644\u0643\u0646 \u0627\u0644\u0639\u0645\u0644\u064a\u0629 \u0644\u0647\u0627 \u0645\u062e\u0627\u0637\u0631\u0647\u0627 \u0648\u062a\u0639\u0642\u064a\u062f\u0627\u062a\u0647\u0627. \u0648\u0641\u064a \u0647\u0630\u0647 \u0627\u0644\u062d\u0627\u0644\u0629 \u064a\u062c\u0628 \u0625\u062c\u0631\u0627\u0621 \u0627\u0644\u0639\u0645\u0644\u064a\u0629\u00a0 \u0645\u0628\u0643\u0631\u0627 \u0642\u0628\u0644 \u062d\u062f\u0648\u062b \u0623\u0636\u0631\u0627\u0631 \u0641\u064a \u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u0645\u062e<\/p>\n<p>3- \u0647\u0646\u0627\u0643 \u0645\u062d\u0627\u0648\u0644\u0627\u062a \u0644\u0645\u0627 \u064a\u0633\u0645\u0649 \u0627\u0644\u0639\u0644\u0627\u062c \u0627\u0644\u062c\u064a\u0646\u064a Gene Therapy\u00a0 \u0648\u0647\u064a \u0641\u064a \u0637\u0648\u0631 \u0627\u0644\u062f\u0631\u0627\u0633\u0629<\/p>\n<p>4- \u0623\u0639\u0636\u0627\u0621 \u0627\u0644\u062c\u0633\u0645 \u0627\u0644\u0645\u062a\u0623\u062b\u0631\u0629 \u0628\u0627\u0644\u0645\u0631\u0636 \u0643\u0627\u0644\u0642\u0644\u0628 \u0645\u062b\u0644\u0627\u00a0 \u064a\u0645\u0643\u0646 \u0627\u0644\u062a\u0639\u0627\u0645\u0644 \u0645\u0639\u0647\u0627 \u0628\u0627\u0644\u0637\u0631\u0642 \u0627\u0644\u0637\u0628\u064a\u0629 \u0627\u0644\u0627\u0639\u062a\u064a\u0627\u062f\u064a\u0629 \u0643\u0645\u0627 \u064a\u0645\u0643\u0646 \u0632\u0631\u0627\u0639\u0629 \u0642\u0631\u0646\u064a\u0629 \u0627\u0644\u0639\u064a\u0646\u00a0 \u0643\u0645\u0627 \u064a\u0645\u0643\u0646 \u0632\u0631\u0627\u0639\u0629 \u0642\u0631\u0646\u064a\u0629 \u0627\u0644\u0639\u064a\u0646 \u0630\u0627 \u0644\u0632\u0645 \u0627\u0644\u0623\u0645\u0631<\/p>\n<p>5- \u064a\u062c\u0628 \u0627\u0644\u0627\u0647\u062a\u0645\u0627\u0645 \u0628\u0627\u0644\u0639\u0644\u0627\u062c \u0627\u0644\u0637\u0628\u064a\u0639\u064a<\/p>\n<p><strong> \u0623\u0628\u0648 \u0627\u062d\u0645\u062f \u0627\u0644\u062b\u0627\u0645\u0646 \u0645\u0646 \u064a\u0646\u0627\u064a\u0631 2005<\/strong><\/p>\n<p><a href=\"http:\/\/www.epaediatrics.org\/vb\/forumdisplay.php?s=f75d714fd6b7d74459f5066885d074df&amp;forumid=22\">\u0627\u0630\u0627 \u0643\u0627\u0646 \u0644\u062f\u064a\u0643 \u0627\u0633\u062a\u0641\u0633\u0627\u0631 \u0623\u0648 \u0633\u0624\u0627\u0644 \u0641\u0637\u0631\u062d\u0629 \u0641\u064a \u0645\u0646\u062a\u062f\u0649 \u0627\u0644\u0648\u0631\u0627\u062b\u0629 \u0627\u0644\u0637\u0628\u064a\u0629<\/a><\/p>\n<p>&nbsp;<\/p>\n<p>&nbsp;<\/p>\n<p>\u0643\u062a\u0628\u0647\u0627 \u0623\u0628\u0648 \u0627\u062d\u0645\u062f ( \u0639\u0645\u0627\u0631 \u0639\u062c\u0648\u0644 )\u00a0 \u062d\u0641\u0638\u0629 \u0627\u0644\u0644\u0647 \u0648 \u0648\u0642\u0627\u0647 \u0645\u0646 \u0643\u0644 \u0633\u0648\u0621<\/p>\n<p>\u0645\u0646 \u0627\u0644\u062f\u0648\u062d\u0629 \u0628\u0642\u0637\u0631<\/p>\n","protected":false},"excerpt":{"rendered":"<p>\u0623\u0645\u0631\u0627\u0636 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631\u064a\u0627\u062a \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629 Mucopolysaccharidosis &nbsp; \u0647\u064a \u0623\u0645\u0631\u0627\u0636 \u0648\u0631\u0627\u062b\u064a\u0629 \u0646\u0627\u062c\u0645\u0629 \u0639\u0646 \u062e\u0644\u0644 \u0641\u064a \u0645\u0627 \u064a\u0633\u0645\u0649 \u0627\u0644\u0644\u064a\u0633\u0648\u0633\u0648\u0645 (lysosome) \u0648\u0647\u0648 \u0627\u0644\u062c\u0632\u0621 \u0627\u0644\u0645\u0633\u0626\u0648\u0644 \u0639\u0646 \u062d\u0631\u0642 recycling) ( \u0627\u0644\u0645\u0648\u0627\u062f \u063a\u064a\u0631 \u0627\u0644\u0645\u0631\u063a\u0648\u0628 \u0641\u064a\u0647\u0627 \u062f\u0627\u062e\u0644 \u0627\u0644\u062e\u0644\u0627\u064a\u0627 \u0648\u062a\u0633\u0645\u0649 \u0623\u0645\u0631\u0627\u0636 \u062a\u062e\u0632\u064a\u0646 ( Storage Disease)\u00a0 \u0644\u0623\u0646 \u0627\u0644\u062c\u0633\u0645 \u064a\u0638\u0644 \u0639\u0627\u062c\u0632\u0627 \u0639\u0646 \u0643\u0646\u0633 \u0648\u062d\u0631\u0642 \u0648\u062a\u0643\u0633\u064a\u0631 \u062a\u0644\u0643 \u0627\u0644\u0645\u0648\u0627\u062f. \u0623\u0645\u0627 \u0643\u064a\u0641\u00a0 \u0644\u0627 \u062a\u0633\u062a\u0637\u064a\u0639 \u0627\u0644\u062e\u0644\u064a\u0629 \u0627\u0644\u062a\u062e\u0644\u0635 \u0645\u0646 \u0645\u0648\u0627\u062f \u0645\u062e\u0632\u0646\u0629 &hellip;<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[30,6],"tags":[],"class_list":["post-1964","post","type-post","status-publish","format-standard","hentry","category-other-metabolic-disorders","category-metabolic"],"_links":{"self":[{"href":"https:\/\/www.werathah.com\/meta\/wp-json\/wp\/v2\/posts\/1964","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.werathah.com\/meta\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.werathah.com\/meta\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.werathah.com\/meta\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/www.werathah.com\/meta\/wp-json\/wp\/v2\/comments?post=1964"}],"version-history":[{"count":1,"href":"https:\/\/www.werathah.com\/meta\/wp-json\/wp\/v2\/posts\/1964\/revisions"}],"predecessor-version":[{"id":3734,"href":"https:\/\/www.werathah.com\/meta\/wp-json\/wp\/v2\/posts\/1964\/revisions\/3734"}],"wp:attachment":[{"href":"https:\/\/www.werathah.com\/meta\/wp-json\/wp\/v2\/media?parent=1964"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.werathah.com\/meta\/wp-json\/wp\/v2\/categories?post=1964"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.werathah.com\/meta\/wp-json\/wp\/v2\/tags?post=1964"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}