{"id":11985,"date":"2018-08-19T20:29:44","date_gmt":"2018-08-19T17:29:44","guid":{"rendered":"http:\/\/www.werathah.com\/special\/?p=11985"},"modified":"2018-11-03T17:12:29","modified_gmt":"2018-11-03T14:12:29","slug":"mucopolysaccharidosis-medical","status":"publish","type":"post","link":"https:\/\/www.werathah.com\/special\/disorders\/mucopolysaccharidosis\/mucopolysaccharidosis-medical\/","title":{"rendered":"\u0623\u0645\u0631\u0627\u0636 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631\u064a\u0627\u062a \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629-\u0645\u0639\u0644\u0648\u0645\u0627\u062a \u0637\u0628\u064a\u0629"},"content":{"rendered":"

\u0623\u0645\u0631\u0627\u0636 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631\u064a\u0627\u062a \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629<\/strong><\/span><\/h1>\n

mucopolysaccharidosis<\/h3>\n

\u0645\u0639\u0644\u0648\u0645\u0627\u062a \u0637\u0628\u064a\u0629<\/span><\/h1>\n

\u0647\u064a \u0623\u0645\u0631\u0627\u0636 \u0648\u0631\u0627\u062b\u064a\u0629 \u0646\u0627\u062c\u0645\u0629 \u0639\u0646 \u062e\u0644\u0644 \u0641\u064a \u0645\u0627 \u064a\u0633\u0645\u0649 \u0627\u0644\u0644\u064a\u0633\u0648\u0633\u0648\u0645 (lysosome) \u0648\u0647\u0648 \u0627\u0644\u062c\u0632\u0621 \u0627\u0644\u0645\u0633\u0626\u0648\u0644 \u0639\u0646 \u0627\u0644\u0645\u0648\u0627\u062f \u063a\u064a\u0631 \u0627\u0644\u0645\u0631\u063a\u0648\u0628 \u0641\u064a\u0647\u0627 \u062f\u0627\u062e\u0644 \u0627\u0644\u062e\u0644\u0627\u064a\u0627. \u0648\u062a\u0635\u0646\u0641 \u0627\u064a\u0636\u0627 \u0645\u0646 \u0623\u0645\u0631\u0627\u0636 \u0627\u0644\u062a\u062e\u0632\u064a\u0646 ( Storage Disease)\u00a0 \u0644\u0623\u0646 \u0627\u0644\u062c\u0633\u0645 \u064a\u0638\u0644 \u0639\u0627\u062c\u0632\u0627 \u0639\u0646 \u062a\u0646\u0638\u064a\u0641 \u0648\u062d\u0631\u0642 \u0648\u062a\u0643\u0633\u064a\u0631 \u062a\u0644\u0643 \u0627\u0644\u0645\u0648\u0627\u062f \u0641\u062a\u062a\u0631\u0627\u0643\u0645 \u0628\u062f\u0627\u062e\u0644 \u0627\u0644\u062e\u0644\u064a\u0629 \u0648 \u0627\u0644\u0627\u0646\u0633\u062c\u0629 \u0641\u062a\u0633\u0628\u0628 \u062e\u0644\u0644 \u0641\u064a \u0648\u0638\u0627\u0626\u0641\u0647\u0627.<\/p>\n

\u0648 \u0627\u0644\u062e\u0644\u064a\u0629 \u062a\u0642\u0648\u0645 \u0628\u0627\u0644\u062a\u062e\u0644\u0635 \u0645\u0646 \u0627\u0644\u0641\u0627\u0626\u0636 \u0645\u0646 \u0627\u0644\u0645\u0648\u0627\u062f \u0648 \u062d\u0631\u0642\u0647\u0627 \u0639\u0646 \u0637\u0631\u064a\u0642 \u062a\u0643\u0633\u064a\u0631\u0647\u0627 \u0628\u0645\u062c\u0645\u0648\u0639\u0629 \u0643\u0628\u064a\u0631\u0629\u00a0\u00a0 \u0645\u0646 \u0627\u0644\u0627\u0646\u0632\u064a\u0645\u0627\u062a ( \u0627\u0644\u062e\u0645\u0627\u0626\u0631) \u0648\u0639\u0646\u062f \u0646\u0642\u0635 \u062e\u0645\u064a\u0631\u0629 \u0645\u0639\u064a\u0646\u0629 \u062a\u062d\u062f\u062b \u0627\u0644\u0627\u0635\u0627\u0628\u0629 \u0628\u0627\u062d\u062f \u0623\u0646\u0648\u0627\u0639 \u0645\u0631\u0636 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631\u064a\u0627\u062a \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629 .<\/p>\n

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\u0647\u0630\u0647 \u0627\u0644\u0623\u0645\u0631\u0627\u0636 \u0631\u063a\u0645 \u0623\u0646\u0647\u0627 \u0642\u062f \u0644\u0627 \u062a\u0643\u0648\u0646 \u0648\u0627\u0636\u062d\u0629 \u0639\u0646\u062f \u0648\u0644\u0627\u062f\u0629 \u0627\u0644\u0637\u0641\u0644 \u0625 \u0644\u0627 \u0623\u0646 \u0639\u0644\u0627\u0645\u0627\u062a\u0647\u0627 \u062a\u0628\u062f\u0623 \u0641\u064a \u0627\u0644\u0638\u0647\u0648\u0631 \u062a\u062f\u0631\u064a\u062c\u064a\u0627 \u0645\u0639 \u062a\u0637\u0648\u0631 \u0627\u0644\u0645\u0631\u0636 \u0627\u0644\u0630\u064a \u064a\u062a\u0637\u0648\u0631 \u0645\u0639 \u0632\u064a\u0627\u062f\u0629 \u0639\u0645\u0631 \u0627\u0644\u0637\u0641\u0644 \u062d\u064a\u062b \u064a\u062a\u0645 \u0625\u062d\u062f\u0627\u062b \u0627\u0644\u0645\u0632\u064a\u062f \u0645\u0646 \u0627\u0644\u0636\u0631\u0631 \u0644\u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u062c\u0633\u0645 \u0644\u0623\u0646 \u0627\u0644\u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u0645\u064a\u062a\u0629 \u062a\u062a\u0631\u0627\u0643\u0645 \u0639\u0644\u064a\u0647\u0627 \u0628\u0645\u0631\u0648\u0631 \u0627\u0644\u0623\u064a\u0627\u0645.<\/p>\n

\u0623\u0645\u0631\u0627\u0636 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631\u064a\u0627\u062a \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629 \u0623\u0648 \u0639\u062f\u064a\u062f \u0627\u0644\u0633\u0643\u0631\u064a\u0627\u062a \u0627\u0644\u0645\u062e\u0627\u0637\u064a (mucopolysaccharidosis) \u062a\u0635\u064a\u0628 \u0648\u0627\u062d\u062f\u0627 \u0645\u0646 \u0628\u064a\u0646 \u0643\u0644 \u062e\u0645\u0633\u0629 \u0648\u0639\u0634\u0631\u064a\u0646 \u0623\u0644\u0641 \u0645\u0648\u0644\u0648\u062f \u062a\u0642\u0631\u064a\u0628\u0627. \u0648\u0647\u064a \u0623\u0645\u0631\u0627\u0636 \u062a\u0633\u0628\u0628 \u0625\u0639\u0627\u0642\u0629 \u062c\u0633\u062f\u064a\u0629 \u0645\u062a\u0637\u0648\u0631\u0629 \u0648\u0645\u0633\u062a\u0645\u0631\u0629 \u0648\u0641\u064a \u0627\u0644\u0639\u062f\u064a\u062f \u0645\u0646 \u0627\u0644\u062d\u0627\u0644\u0627\u062a \u062a\u0648\u062c\u062f \u0625\u0639\u0627\u0642\u0629 \u0639\u0642\u0644\u064a\u0629 \u0634\u062f\u064a\u062f\u0629 \u0648\u0639\u0627\u062f\u0629 \u064a\u0645\u0648\u062a \u0627\u0644\u0645\u0635\u0627\u0628\u0648\u0646 \u0648\u0647\u0645 \u0641\u064a \u0639\u0645\u0631 \u0627\u0644\u0637\u0641\u0648\u0644\u0629 \u0644\u0643\u0646 \u0647\u0646\u0627\u0643 \u0627\u0633\u062a\u062b\u0646\u0627\u0621\u0627\u062a \u064a\u0637\u0648\u0644 \u0641\u064a\u0647\u0627 \u0627\u0644\u0639\u0645\u0631.<\/p>\n

\u0623\u0642\u0633\u0627\u0645 \u0645\u0631\u0636 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631 \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629 <\/strong><\/p>\n

\u064a\u0646\u0642\u0633\u0645 \u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 \u0625\u0644\u0649 \u0633\u0628\u0639\u0629 \u0623\u0642\u0633\u0627\u0645 \u0648\u064a\u0633\u0645\u0649 \u0643\u0644 \u0646\u0648\u0639 \u0628\u0627\u0633\u0645 \u0627\u0644\u0637\u0628\u064a\u0628 \u0627\u0644\u0630\u064a \u0627\u0643\u062a\u0634\u0641\u0647.<\/p>\n

\u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0623\u0648\u0644\u00a0\u00a0 MPS-1<\/p>\n

\u0648\u0647\u0630\u0627 \u0627\u0644\u0646\u0648\u0639 \u064a\u0646\u0642\u0633\u0645 \u0625\u0644\u0649 \u062b\u0644\u0627\u062b\u0629 \u0623\u0642\u0633\u0627\u0645 \u062d\u0633\u0628 \u0634\u062f\u0629 \u0627\u0644\u0645\u0631\u0636 : \u0645\u062a\u0644\u0627\u0632\u0645\u0629\u00a0 \u0647\u064a\u0631\u0644\u0648\u0631\u00a0(\u0625\u0635\u0627\u0628\u0629 \u0634\u062f\u064a\u062f\u0629) \u0648 \u0645\u062a\u0644\u0627\u0632\u0645\u0629\u00a0 \u0647\u064a\u0631\u0644\u0631 \u0633\u0643\u064a ( \u0625\u0635\u0627\u0628\u0629 \u0645\u062a\u0648\u0633\u0637\u0629) \u0648 \u0645\u062a\u0644\u0627\u0632\u0645\u0629\u00a0 \u0633\u0643\u064a (\u0623\u062d\u064a\u0627\u0646\u0627 \u062a\u0643\u062a\u0628 \u062a\u0634\u0627\u064a). (\u0625\u0635\u0627\u0628\u0629 \u062e\u0641\u064a\u0641\u0629)<\/p>\n

\u0647\u0630\u0647 \u0627\u0644\u0627\u0646\u0648\u0627\u0639 \u0627\u0644\u062b\u0644\u0627\u062b \u0647\u064a \u0646\u062a\u064a\u062c\u0629 \u0644\u0646\u0642\u0635 \u0627\u0646\u0632\u064a\u0645 \u0648\u0627\u062d\u062f \u0644\u0643\u0646 \u062f\u0631\u062c\u0629 \u0627\u0644\u0646\u0642\u0635 \u0645\u062a\u0641\u0627\u0648\u062a\u0647 \u0628\u064a\u0646\u0647\u0627 \u0644\u0630\u0644\u0643 \u0627\u0644\u0627\u0635\u0627\u0628\u0629 \u062a\u0643\u0648\u0646 \u0645\u062e\u062a\u0644\u0641\u0629.<\/p>\n

\u0648\u0642\u062f \u0623\u062e\u0630 \u0627\u0644\u0645\u0631\u0636 \u0627\u0633\u0645\u0647- \u0647\u064a\u0631\u0644\u0648\u0631- \u0645\u0646 \u0627\u0644\u0637\u0628\u064a\u0628 \u062c\u064a\u0631\u062a\u0631\u062f \u0647\u064a\u0631\u0644\u0648\u0631\u00a0\u00a0\u00a0 Gertrud Hurler \u0627\u0644\u0630\u064a \u0648\u0635\u0641 \u0637\u0641\u0644\u0627 \u0648\u0637\u0641\u0644\u0629 \u0628\u0639\u0644\u0627\u0645\u0627\u062a \u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 \u0641\u064a \u0627\u0644\u0639\u0627\u0645 \u0623\u0644\u0641 \u0648\u062a\u0633\u0639\u0645\u0627\u0626\u0629 \u0648\u062a\u0633\u0639\u0629 \u0639\u0634\u0631. \u0648\u0641\u064a \u0639\u0627\u0645\u00a0 \u0623\u0644\u0641 \u0648\u062a\u0633\u0639\u0645\u0627\u0626\u0629 \u0648\u0627\u062b\u0646\u064a\u0646 \u0648\u0633\u062a\u064a\u0646 \u0643\u062a\u0628 \u0627\u0644\u0627\u0633\u062a\u0634\u0627\u0631\u064a \u0641\u064a \u0623\u0645\u0631\u0627\u0636 \u0627\u0644\u0639\u064a\u0648\u0646 \u062f\u0643\u062a\u0648\u0631 \u0633\u0643\u064a\u00a0\u00a0 Schie\u00a0 \u0639\u0646 \u0645\u0631\u0636\u0649 \u0643\u0627\u0646\u062a \u0625\u0635\u0627\u0628\u0627\u062a\u0647\u0645 \u0623\u0642\u0644 \u0636\u0631\u0627\u0648\u0629. \u0623\u0645\u0627 \u0627\u0644\u0645\u0631\u0636\u0649 \u0627\u0644\u0630\u064a\u0646 \u0644\u0627 \u064a\u0648\u0635\u0641\u0648\u0646 \u0628\u0623\u0646 \u0625\u0635\u0627\u0628\u062a\u0647\u0645 \u0634\u062f\u064a\u062f\u0629 \u0623\u0648 \u062e\u0641\u064a\u0641\u0629 \u0641\u0625\u0646\u0647\u0645 \u064a\u0639\u0631\u0641\u0648\u0646 \u0628\u062f\u0645\u062c \u0627\u0644\u0627\u0633\u0645\u064a\u0646 \u0645\u0639\u0627 \u0647\u064a\u0631\u0644\u0648\u0631- \u0633\u0643\u064a Hurler\/Schie\u00a0 .<\/p>\n

 <\/p>\n\n\n\n\n\n\n\n\n\n\n\n\n\n\n\n\n\n
\n

\u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0631\u0626\u064a\u0633\u064a<\/span><\/strong><\/h3>\n<\/td>\n

\n

\u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0641\u0631\u0639\u064a<\/strong><\/span><\/h3>\n<\/td>\n

\n

\u0627\u0644\u0639\u0645\u0631 \u0639\u0646\u062f \u0627\u0644\u062a\u0634\u062e\u064a\u0635<\/strong><\/span><\/h3>\n<\/td>\n

\n

\u0627\u0644\u0639\u0645\u0631 \u0627\u0644\u0645\u062a\u0648\u0642\u0639<\/strong><\/span><\/h3>\n<\/td>\n

\n

\u0646\u0633\u0628\u0629 \u0644\u0627\u0646\u062a\u0634\u0627\u0631<\/strong><\/span><\/h3>\n<\/td>\n

\n

\u0627\u0644\u0642\u062f\u0631\u0627\u062a \u0627\u0644\u0639\u0642\u0644\u064a\u0629<\/strong><\/span><\/h3>\n<\/td>\n

\n

\u0627\u0644\u0639\u0644\u0627\u062c<\/strong><\/span><\/h3>\n<\/td>\n<\/tr>\n

\u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0623\u0648\u0644 \u0647\u064a\u0644\u0631<\/strong><\/span><\/td>\n\u0647\u064a\u0644\u0631
\n(MPS IH)<\/td>\n		\u0634\u062f\u064a\u062f 6-24 \u0634\u0647\u0631<\/td>\n\u0639\u0627\u062f\u0629 \u0623\u0642\u0644 \u0645\u0646 10 \u0633\u0646\u0648\u0627\u062a<\/td>\n\u0648\u0627\u062d\u062f \u0644\u0643\u0644 \u0627\u0644\u0641 \u0645\u0648\u0644\u0648\u062f<\/td>\n\u0645\u062a\u0623\u062e\u0631 \u0628\u0639\u062f 3-4 \u0633\u0646\u0648\u0627\u062a<\/td>\n\u0632\u0631\u0627\u0639\u0629 \u0627\u0644\u0646\u062e\u0627\u0639 \u0627\u0642\u0644 \u0645\u0646 \u0633\u0646\u064a\u062a\u0646. \u0627\u0644\u062a\u0639\u0648\u064a\u0636 \u0628\u0627\u0644\u0625\u0646\u0632\u064a\u0645<\/td>\n<\/tr>\n
\u00a0\u062a\u0634\u0627\u064a- \u0647\u064a\u0631\u0644\u0631 Hurler-scheie\u00a0 (MPS IH\/S)<\/td>\n\u0623\u0642\u0644 \u0634\u062f\u0647 3-8 \u0633\u0646\u0648\u0627\u062a<\/td>\n\u0627\u0643\u062b\u0631 \u0645\u0646 20 \u0633\u0646\u0629<\/td>\n\u0637\u0628\u064a\u0639\u064a<\/td>\n\u0639\u0644\u0627\u062c \u0627\u0644\u0627\u0639\u0631\u0627\u0636\u00a0 \u0648 \u0627\u0644\u062a\u0639\u0648\u064a\u0636 \u0628\u0627\u0644\u0625\u0646\u0632\u064a\u0645<\/td>\n<\/tr>\n
\u062a\u0634\u0627\u064a
\nScheie (MPS IS)<\/td>\n		\u0627\u0643\u062b\u0631 \u0645\u0646 5 \u0633\u0646\u0648\u0627\u062a<\/td>\n\u0637\u0628\u064a\u0639\u064a<\/td>\n\u0637\u0628\u064a\u0639\u064a<\/td>\n\u0639\u0644\u0627\u062c \u0627\u0644\u0627\u0639\u0631\u0627\u0636\u00a0 \u0648 \u0627\u0644\u062a\u0639\u0648\u064a\u0636 \u0628\u0627\u0644\u0625\u0646\u0632\u064a\u0645<\/td>\n<\/tr>\n
\u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u062b\u0627\u0646\u064a<\/span><\/strong><\/p>\n

\u0647\u0646\u062a\u0631<\/span><\/strong><\/td>\n

MPS IIA<\/td>\n\u0627\u0644\u0634\u062f\u064a\u062f \u0645\u0646 18 \u0634\u0647\u0631 \u0627\u0644\u0649 4 \u0633\u0646\u0648\u0627\u062a<\/td>\n\u064a\u0639\u062a\u0645\u062f \u0639\u0644\u0649 \u0627\u0644\u0634\u062f\u0629 10-15 \u0633\u0646\u0629<\/td>\n\u0648\u0627\u062d\u062f \u0645\u0635\u0627\u0628 \u0644\u0643\u0644 140 \u0627\u0644\u0649 150 \u0627\u0644\u0641 \u0630\u0643\u0631<\/td>\n\u0645\u062a\u0623\u062e\u0631 \u0628\u0639\u062f2-3 \u0633\u0646\u0648\u0627\u062a<\/td>\n\u0639\u0644\u0627\u062c \u0627\u0644\u0627\u0639\u0631\u0627\u0636\u00a0 \u0648 \u0627\u0644\u062a\u0639\u0648\u064a\u0636 \u0628\u0627\u0644\u0625\u0646\u0632\u064a\u0645<\/td>\n<\/tr>\n
MPS IIB<\/td>\n\u0627\u0643\u062b\u0631 \u0645\u0646 5 \u0633\u0646\u0648\u0627\u062a<\/td>\n20 -60 \u0633\u0646\u0629<\/td>\n\u0637\u0628\u064a\u0639\u064a<\/td>\n\u0639\u0644\u0627\u062c \u0627\u0644\u0627\u0639\u0631\u0627\u0636\u00a0 \u0648 \u0627\u0644\u062a\u0639\u0648\u064a\u0636 \u0628\u0627\u0644\u0625\u0646\u0632\u064a\u0645<\/td>\n<\/tr>\n
\u0633\u0627\u0646 \u0641\u064a\u0644\u064a\u0628\u0648<\/span><\/strong><\/td>\nMPS IIIA<\/td>\n\u0633\u0646\u0629 \u0627\u0644\u0649 \u0633\u0646\u062a\u064a\u0646 \u0644\u0644\u0646\u0648\u0639 \u0627\u0644\u0634\u062f\u064a\u062f \u0648 \u0627\u0644\u0627\u0642\u0644 \u0634\u062f\u0629 \u0642\u062f \u064a\u0638\u0647\u0631 \u0641\u064a \u0627\u0644\u0643\u0628\u0631 \u0623\u0648 \u062d\u062a\u0649 \u0628\u0639\u062f 50 \u0633\u0646\u0629<\/td>\n\u0644\u0644\u0646\u0648\u0639 \u0627\u0644\u0634\u062f\u064a\u062f \u0628\u064a\u064620-40 \u0633\u0646\u0629 \u0644\u0644\u0646\u0648\u0639 \u0627\u0644\u062e\u0641\u064a\u0641 40-70 \u0633\u0646\u0629<\/td>\n\u0637\u0641\u0644 \u0644\u0643\u0644 70 \u0627\u0644\u0649 90 \u0627\u0644\u0641 \u0645\u0648\u0644\u0648\u062f<\/td>\n\u0627\u0644\u062a\u0623\u062e\u0631 \u0628\u0639\u062f \u0633\u0646\u064a\u062a\u0646 \u0645\u0646 \u0627\u0644\u0639\u0645\u0631<\/td>\n\u0639\u0644\u0627\u062c \u0627\u0644\u0627\u0639\u0631\u0627\u0636\u00a0 \u0648 \u0627\u0644\u062a\u0639\u0648\u064a\u0636 \u0628\u0627\u0644\u0625\u0646\u0632\u064a\u0645<\/td>\n<\/tr>\n
MPS IIIB<\/td>\n\u0639\u0644\u0627\u062c \u0627\u0644\u0627\u0639\u0631\u0627\u0636<\/td>\n<\/tr>\n
MPS IIIC<\/td>\n\u0639\u0644\u0627\u062c \u0627\u0644\u0627\u0639\u0631\u0627\u0636\u00a0 \u0648 \u0627\u0644\u062a\u0639\u0648\u064a\u0636 \u0628\u0627\u0644\u0625\u0646\u0632\u064a\u0645<\/td>\n<\/tr>\n
MPS IIID<\/td>\n\u0639\u0644\u0627\u062c \u0627\u0644\u0627\u0639\u0631\u0627\u0636<\/td>\n<\/tr>\n
\u0645\u0648\u0631\u0643\u064a\u0648<\/strong><\/span><\/td>\nMPS IV Morquio<\/td>\n\u0633\u0646\u0629 \u0627\u0644\u0649 \u062b\u0644\u0627\u062b \u0633\u0646\u0648\u0627\u062a<\/td>\n\u0644\u0644\u0646\u0648\u0639 \u0627\u0644\u0634\u062f\u064a\u062f 2-3 \u0633\u0646\u0648\u0627\u062a<\/p>\n

\u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u062e\u0641\u064a\u0641 60-70 \u0633\u0646\u0629<\/td>\n

\u0648\u0627\u062c\u062f \u0645\u0635\u0627\u0628 \u0644\u0643\u0644 200 \u0627\u0644\u0641 \u0645\u0648\u0644\u0648\u062f<\/td>\n\u0637\u0628\u064a\u0639\u064a<\/td>\n\u0639\u0644\u0627\u062c \u0627\u0644\u0627\u0639\u0631\u0627\u0636\u00a0 \u0648 \u0627\u0644\u062a\u0639\u0648\u064a\u0636 \u0628\u0627\u0644\u0625\u0646\u0632\u064a\u0645<\/td>\n<\/tr>\n
MPS IVB<\/td>\n\u0639\u0644\u0627\u062c \u0627\u0644\u0627\u0639\u0631\u0627\u0636<\/td>\n<\/tr>\n
\u0645\u0627\u0631\u062a\u0648 \u0644\u0627\u0645\u064a<\/span><\/strong><\/td>\nMPS VI Maroteaux-Lamy<\/td>\n2-3 \u0633\u0646\u0648\u0627\u062a<\/td>\n\u0644\u0644\u0646\u0648\u0639 \u0627\u0644\u0634\u062f\u064a\u062f \u062d\u0648\u0627\u0644\u064a 20 \u0633\u0646\u0629 \u0644\u0644\u062e\u0641\u064a\u0641 \u0627\u0643\u062b\u0631<\/td>\n\u0645\u0635\u0627\u0628 \u0644\u0643\u0644 240-300 \u0627\u0644\u0641 \u0645\u0648\u0644\u0648\u062f<\/td>\n\u0637\u0628\u064a\u0639\u064a<\/td>\n\u0639\u0644\u0627\u062c \u0627\u0644\u0627\u0639\u0631\u0627\u0636\u00a0 \u0648 \u0627\u0644\u062a\u0639\u0648\u064a\u0636 \u0628\u0627\u0644\u0625\u0646\u0632\u064a\u0645<\/td>\n<\/tr>\n
\u0633\u0644\u0627\u064a<\/strong><\/span><\/td>\nMPS VII Sly<\/td>\n0-7 \u0633\u0646\u0648\u0627\u062a<\/td>\n\u0645\u0646 \u0627\u0634\u0647\u0631 \u0627\u0644\u0649 20-40 \u0633\u0646\u0629<\/td>\n\u0645\u0635\u0627\u0628 \u0644\u0643\u0644 240 \u0627\u0644\u0641 \u0645\u0648\u0644\u0648\u062f<\/td>\n\u064a\u062a\u0623\u062e\u0631 \u0645\u0646 \u0627\u0644\u0628\u062f\u0627\u064a\u0629<\/td>\n\u0639\u0644\u0627\u062c \u0627\u0644\u0627\u0639\u0631\u0627\u0636\u00a0 \u0648 \u0627\u0644\u062a\u0639\u0648\u064a\u0636 \u0628\u0627\u0644\u0625\u0646\u0632\u064a\u0645<\/td>\n<\/tr>\n
\u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u062a\u0627\u0633\u0639<\/strong><\/span><\/td>\nMPS IX Hyaluronidase deficiency<\/td>\n\u061f<\/td>\n\u063a\u064a\u0631 \u0645\u0639\u0631\u0648\u0641<\/td>\n\u062d\u0627\u0644\u0629 \u0648\u0627\u062d\u062f\u0629 \u0645\u0634\u062e\u0635\u0629<\/td>\n\u061f<\/td>\n\u0639\u0644\u0627\u062c \u0627\u0644\u0623\u0639\u0631\u0627\u0636<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n

\u0627\u0644\u062a\u0634\u0627\u0628\u0647 \u0648 \u0627\u0644\u0641\u0631\u0648\u0642\u0627\u062a \u0628\u064a\u0646 \u0627\u0644\u0623\u0646\u0648\u0627\u0639<\/strong><\/span><\/h1>\n

\u00a0<\/strong><\/p>\n

\u062a\u062a\u0634\u0627\u0628\u0647\u00a0 \u0627\u0645\u0631\u0627\u0636 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631\u064a\u0627\u062a \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629 \u0641\u064a\u0645\u0627 \u0628\u064a\u0646\u0647\u0627 \u0641\u064a \u0627\u0644\u0623\u0639\u0631\u0627\u0636. \u0648 \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0623\u0648\u0644 \u064a\u062a\u0637\u0648\u0631 \u0628\u0634\u0643\u0644 \u0633\u0631\u064a\u0639 \u0645\u0642\u0627\u0631\u0646\u0629 \u0628\u0627\u0644\u0623\u0646\u0648\u0627\u0639 \u0627\u0644\u0623\u062e\u0631\u0649. \u0648\u0647\u0646\u0627\u0643 \u0641\u0631\u0648\u0642\u0627\u062a \u0641\u064a\u0645\u0627 \u0628\u064a\u0646\u0647\u0627 \u0641\u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0631\u0627\u0628\u0639 \u0639\u0644\u0649 \u0633\u0628\u064a\u0644 \u0627\u0644\u0645\u062b\u0627\u0644 \u0647\u0648 \u0645\u062e\u062a\u0644\u0641 \u0639\u0646 \u0628\u0642\u064a\u0629 \u0627\u0644\u0623\u0646\u0648\u0627\u0639 \u0641\u0627\u0644\u0642\u062f\u0631\u0627\u062a \u0627\u0644\u0639\u0642\u0644\u064a\u0629 \u0644\u0627 \u062a\u062a\u0623\u062b\u0631 \u0630\u0627 \u062a\u0623\u062b\u0631\u062a \u062a\u062a\u0623\u062b\u0631 \u0628\u0634\u0643\u0644 \u062e\u0641\u064a\u0641. \u0643\u0645\u0627 \u0623\u0646 \u0627\u0644\u0642\u0631\u0646\u064a\u0629 \u0644\u0627 \u064a\u062d\u062f\u062b \u0644\u0647\u0627 \u0639\u0627\u062a\u0645\u0629 \u0641\u064a \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u062b\u0627\u0646\u064a \u0648\u0644\u0627 \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0631\u0627\u0628\u0639.<\/strong><\/p>\n

\u0642\u0635\u0631 \u0627\u0644\u0642\u0627\u0645\u0629 \u0634\u064a\u0621 \u0634\u0627\u0626\u0639 \u0628\u064a\u0646 \u062c\u0645\u064a\u0639 \u0627\u0644\u0623\u0646\u0648\u0627\u0639 \u0648 \u0642\u062f \u064a\u062a\u0648\u0642\u0641 \u0627\u0644\u0637\u0648\u0644 \u0641\u064a \u0627\u0644\u0632\u064a\u0627\u062f\u0629 \u0639\u0646\u062f \u0633\u0646 \u0627\u0644\u062b\u0627\u0644\u062b\u0629 \u0645\u0646 \u0627\u0644\u0639\u0645\u0631. \u0645\u0639 \u0623\u0646 \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u062b\u0627\u0644\u062b \u0642\u062f \u064a\u0633\u062a\u0645\u0631 \u0646\u0645\u0648 \u0627\u0644\u0623\u0637\u0641\u0627\u0644 \u0627\u0644\u0649 \u0633\u0646 \u0627\u0644\u0639\u0627\u0634\u0631\u0629 \u0645\u0646 \u0627\u0644\u0639\u0645\u0631.<\/strong><\/p>\n

\u0645\u0646 \u0627\u0644\u0645\u0634\u0627\u0643\u0644 \u0627\u0644\u0635\u062d\u064a\u0629 \u0627\u0644\u0645\u0647\u0645\u0629 \u0648 \u0627\u0644\u062a\u064a \u062a\u0634\u0643\u0644 \u062e\u0637\u0648\u0631\u0629 \u0647\u064a \u0645\u0634\u0627\u0643\u0644 \u0627\u0644\u0641\u0642\u0631\u0627\u062a \u0627\u0644\u0639\u0646\u0642\u064a\u0629 \u0641\u0642\u062f \u064a\u0643\u0648\u0646 \u0641\u064a\u0647\u0627 \u0627\u0631\u062a\u062e\u0627\u0621 \u0641\u064a \u0627\u0644\u0641\u0642\u0631\u0627\u062a \u0627\u0644\u0639\u0644\u0648\u064a\u0629 \u0623\u0648 \u062a\u0636\u064a\u0642 \u0641\u064a \u0645\u062c\u0631\u0649 \u0627\u0644\u0639\u0645\u0648\u062f \u0627\u0644\u0641\u0642\u0631\u064a \u0641\u064a\u0633\u0628\u0628 \u0636\u063a\u0637 \u0639\u0644\u0649 \u0627\u0644\u062d\u0628\u0644 \u0627\u0644\u0634\u0648\u0643\u064a . \u0648\u0645\u0646 \u0627\u0644\u0645\u0634\u0627\u0643\u0644 \u0627\u0644\u0634\u0627\u0626\u0639\u0629 \u0648\u0627\u0644\u0645\u0634\u062a\u0631\u0643\u0629 \u0628\u064a\u0646 \u0627\u0644\u0627\u0646\u0648\u0627\u0639 \u0647\u0648 \u062a\u064a\u0628\u0633 \u0627\u0644\u0645\u0641\u0627\u0635\u0644 \u0623\u0648 \u0627\u0631\u062a\u062e\u0627\u0621 \u0648 \u0644\u064a\u0648\u0646 \u0641\u064a \u0627\u0644\u0645\u0641\u0627\u0635\u0644 \u0643\u0645\u0627 \u0647\u0648 \u0627\u0644\u062d\u0627\u0644 \u0641\u064a \u0645\u0631\u0636 \u0645\u0627\u0631\u0643\u064a\u0648.<\/strong><\/p>\n

\u0648 \u0641\u064a \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u062b\u0627\u0644\u062b \u0641\u0627\u0646 \u0627\u0644\u0642\u062f\u0631\u0627\u062a \u0627\u0644\u0639\u0642\u0644\u064a\u0629 \u062a\u0628\u062f\u0623 \u0628\u0627\u0644\u062a\u0623\u062e\u0631 \u0641\u064a \u0645\u0646\u062a\u0635\u0641 \u0627\u0644\u0633\u0646\u0629 \u0627\u0644\u062b\u0627\u0646\u064a\u0629 \u0648 \u0627\u0644\u062b\u0627\u0644\u062b\u0629 \u0645\u0646 \u0627\u0644\u0639\u0645\u0631 \u0623\u064a \u062d\u0648\u0627\u0644\u064a \u0639\u0634\u0631 \u0633\u0646\u0648\u0627\u062a \u0642\u0628\u0644 \u0623\u0646 \u062a\u062a\u0623\u062b\u0631 \u0627\u0644\u0645\u0647\u0627\u0631\u0627\u062a \u0627\u0644\u062d\u0631\u0643\u064a\u0629.<\/strong><\/p>\n

\u00a0\u062a\u0628\u062f\u0623 \u0645\u0634\u0627\u0643\u0644 \u0627\u0644\u0646\u0648\u0645 \u0648\u0627\u0644\u0633\u0644\u0648\u0643 \u0639\u0646\u062f \u0639\u0645\u0631 3 \u0625\u0644\u0649 4 \u0633\u0646\u0648\u0627\u062a \u062a\u0642\u0631\u064a\u0628\u064b\u0627. \u0648 \u0642\u062f \u062a\u0643\u0648\u0646 \u0645\u0644\u0627\u0645\u062d \u0627\u0644\u0648\u062c\u0647 \u0642\u0631\u064a\u0628\u0629 \u0645\u0646 \u0627\u0644\u0637\u0628\u064a\u0639\u064a \u0648 \u0642\u062f \u0644\u0627 \u064a\u062a\u0645 \u062a\u0634\u062e\u064a\u0635 \u0627\u0644\u062d\u0627\u0644\u0627\u062a \u0627\u0644\u0627 \u0645\u062a\u0623\u062e\u0631\u0629 \u062e\u0627\u0635\u0629 \u0641\u064a \u0628\u0639\u0636 \u0627\u0644\u0623\u0646\u0648\u0627\u0639 \u0648 \u062a\u0638\u0647\u0631 \u0627\u0644\u0627\u0639\u0631\u0627\u0636 \u0641\u0642\u0637 \u0628\u0633\u0644\u0648\u0643\u064a\u0627\u062a \u063a\u064a\u0631 \u0645\u0631\u063a\u0648\u0628\u0629 \u0645\u062b\u0644 \u062a\u0634\u062a\u062a \u0627\u0644\u0627\u0646\u062a\u0628\u0627\u0647 \u0623\u0648 \u0627\u0644\u062a\u0648\u062d\u062f \u0648 \u0639\u062f\u0645 \u0627\u0644\u062a\u0631\u0643\u064a\u0632 \u0648 \u062a\u0623\u062e\u0631 \u0627\u0644\u0646\u0645\u0648<\/strong><\/p>\n


\n<\/strong>\u0637\u0628\u064a\u0639\u0629 \u0627\u0644\u0645\u0631\u0636 \u0648\u0623\u0633\u0628\u0627\u0628\u0647<\/span><\/h2>\n

\u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631\u064a\u0627\u062a \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629 \u00a0\u0647\u064a \u0633\u0644\u0633\u0644\u0629 \u0637\u0648\u064a\u0644\u0629 \u0627\u0644\u0642\u0637\u0639 \u0627\u0644\u0643\u064a\u0645\u064a\u0627\u0626\u064a\u0629 \u0645\u0631\u0643\u0628\u0629 \u0645\u0646 \u0645\u0627\u062f\u0629 \u0633\u0643\u0631\u064a\u0629 \u0648 \u0645\u062e\u0627\u0637\u064a\u0629 \u062a\u0633\u062a\u062e\u062f\u0645 \u0641\u064a \u0628\u0646\u0627\u0621\u00a0 \u0627\u0644\u0646\u0633\u064a\u062c \u0627\u0644\u0636\u0627\u0645 . \u0648 \u0643\u0644\u0645\u0629 \u0633\u0643\u0631\u0627\u064a\u062f (saccharide) \u0647\u0648 \u0627\u0635\u0637\u0644\u0627\u062d \u0639\u0627\u0645 \u064a\u0637\u0644\u0642 \u0639\u0644\u0649 \u062c\u0632\u064a\u0621 \u0627\u0644\u0633\u0643\u0631 \u0648 \u0643\u0644\u0645\u0629 \u0628\u0648\u0644\u064a (Poly) \u062a\u0639\u0646\u064a \u0645\u062a\u0639\u062f\u062f \u0623\u0648 \u0639\u062f\u064a\u062f\u0627\u062a\u060c\u0648 \u0648\u0628\u0647\u0630\u0627 \u064a\u062c\u064a\u0621 \u0627\u0644\u0627\u0633\u0645 \u0645\u0646 \u0627\u0644\u0643\u0644\u0645\u0627\u062a \u0627\u0644\u062b\u0644\u0627\u062b mucopolysaccharidosis .<\/p>\n

\u0647\u0646\u0627\u0643 \u0639\u0645\u0644\u064a\u0629 \u0645\u0633\u062a\u0645\u0631\u0629 \u0641\u064a \u0627\u0644\u062c\u0633\u0645 \u0644\u062a\u063a\u064a\u064a\u0631 \u0627\u0644\u0645\u0648\u0627\u062f \u0627\u0644\u062a\u064a \u062a\u0645 \u0627\u0633\u062a\u062e\u062f\u0627\u0645\u0647\u0627 \u0648\u062d\u0631\u0642\u0647\u0627 \u0628\u063a\u0631\u0636 \u0627\u0644\u062a\u062e\u0644\u0635 \u0645\u0646\u0647\u0627. \u0627\u0644\u0623\u0637\u0641\u0627\u0644 \u0627\u0644\u0645\u0635\u0627\u0628\u0648\u0646 \u0628\u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0627\u0648\u0644 \u0639\u0644\u0649 \u0633\u0628\u064a\u0644 \u0627\u0644\u0645\u062b\u0627\u0644 \u064a\u0643\u0648\u0646 \u0644\u062f\u064a\u0647\u0645 \u0646\u0642\u0635 \u0641\u064a \u00a0\u0625\u0646\u0632\u064a\u0645 \u064a\u0633\u0645\u0649\u00a0\u00a0 Alpha-L-Iduronidase\u00a0 \u0648\u0647\u0648 \u0627\u0644\u0625\u0646\u0632\u064a\u0645 \u0627\u0644\u0645\u0633\u0626\u0648\u0644 \u0639\u0646 \u062d\u0631\u0642 \u062c\u0632\u064a\u0626\u0627\u062a \u0627\u0644\u0633\u0643\u0631 \u0627\u0644\u0645\u0633\u0645\u0627\u0629 dermatan sulfate and heparan sulfate glycosaminoglycans \u0648\u0647\u064a \u062a\u062e\u062a\u0635\u0631 \u0639\u0645\u0648\u0645\u0627 \u0628\u0627\u0633\u0645\u00a0 GAGs.\u0648\u0647\u0630\u0647 \u0627\u0644\u062c\u0632\u064a\u0626\u0627\u062a \u0627\u0644\u062a\u064a \u0644\u0627 \u064a\u062a\u0645 \u062d\u0631\u0642\u0647\u0627 \u0648\u062a\u0643\u0633\u064a\u0631\u0647\u0627 \u0628\u0635\u0648\u0631\u0629 \u0643\u0627\u0645\u0644\u0629 \u062a\u0628\u0642\u0649 \u0645\u062e\u0632\u0646\u0629 \u0641\u064a \u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u062c\u0633\u0645 \u0645\u0633\u0628\u0628\u0629 \u062f\u0645\u0627\u0631\u0627 \u0645\u0633\u062a\u0645\u0631\u0627 \u0648\u0645\u062a\u0635\u0627\u0639\u062f\u0627 \u0648\u0645\u062a\u0633\u0639 \u0627\u0644\u0646\u0637\u0627\u0642.\u00a0 \u0627\u0644\u0623\u0637\u0641\u0627\u0644 \u062d\u062f\u064a\u062b\u0648 \u0627\u0644\u0648\u0644\u0627\u062f\u0629 \u064a\u0645\u0643\u0646 \u0623\u0646 \u062a\u0638\u0647\u0631 \u0639\u0644\u064a\u0647\u0645 \u0639\u0644\u0627\u0645\u0627\u062a \u0637\u0641\u064a\u0641\u0629 \u0644\u0644\u0645\u0631\u0636. \u0648\u0644\u0643\u0646 \u0628\u0627\u0632\u062f\u064a\u0627\u062f \u0627\u0644\u062f\u0645\u0627\u0631 \u0627\u0644\u0630\u064a \u064a\u0644\u062d\u0642 \u0628\u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u062c\u0633\u0645 \u062a\u0628\u062f\u0623 \u0627\u0644\u0623\u0639\u0631\u0627\u0636 \u0641\u064a \u0627\u0644\u0648\u0636\u0648\u062d \u0623\u0643\u062b\u0631 \u0641\u0623\u0643\u062b\u0631.<\/p>\n

\u0647\u0644 \u064a\u0645\u0643\u0646 \u0627\u0644\u062a\u0645\u064a\u064a\u0632 \u062a\u0645\u0627\u0645\u0627 \u0628\u064a\u0646 \u0623\u0642\u0633\u0627\u0645 \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0623\u0648\u0644 \u0645\u0646 \u0639\u062f\u064a\u062f \u0627\u0644\u0633\u0643\u0631 \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u061f<\/strong><\/p>\n

\u062a\u062a\u0631\u0627\u0648\u062d \u0623\u0639\u0631\u0627\u0636 \u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 \u0645\u0627 \u0628\u064a\u0646 \u0627\u0644\u0634\u062f\u064a\u062f\u0629 \u0625\u0644\u0649 \u0623\u0639\u0631\u0627\u0636 \u062e\u0641\u064a\u0641\u0629. \u0648\u0647\u0646\u0627\u0643 \u0641\u0631\u0648\u0642 \u0634\u0627\u0633\u0639\u0629 \u0641\u064a \u0647\u0630\u0647 \u0627\u0644\u0623\u0639\u0631\u0627\u0636 \u0628\u064a\u0646 \u0627\u0644\u0645\u0631\u0636\u0649. \u0648\u0647\u0630\u0627 \u064a\u062c\u0639\u0644 \u0641\u064a \u0628\u0639\u0636 \u0627\u0644\u0623\u062d\u064a\u0627\u0646 \u062a\u0635\u0646\u064a\u0641 \u0627\u0644\u0645\u0631\u064a\u0636 \u0648\u0648\u0636\u0639\u0647 \u0636\u0645\u0646 \u0642\u0633\u0645 \u0645\u0639\u064a\u0646 \u0645\u0646 \u0623\u0642\u0633\u0627\u0645 \u0647\u0630\u0627 \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0623\u0648\u0644 \u0623\u0645\u0631\u0627 \u0635\u0639\u0628\u0627. \u0648\u0631\u063a\u0645 \u0623\u0646 \u0627\u0644\u0645\u0635\u0627\u0628\u064a\u0646 \u0628\u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u062e\u0641\u064a\u0641 \u062a\u0643\u0648\u0646 \u0642\u062f\u0631\u0627\u062a\u0647\u0645 \u0627\u0644\u0639\u0642\u0644\u064a\u0629 \u0639\u0627\u062f\u064a\u0629 \u0625\u0644\u0627 \u0623\u0646\u0647\u0645 \u0641\u064a \u0630\u0627\u062a \u0627\u0644\u0648\u0642\u062a\u00a0 \u0642\u062f \u064a\u0643\u0648\u0646\u0648\u0646 \u0645\u0635\u0627\u0628\u064a\u0646 \u0628\u0623\u0639\u0631\u0627\u0636 \u0645\u062a\u0628\u0627\u064a\u0646\u0629 \u0645\u0627 \u0628\u064a\u0646 \u0627\u0644\u062d\u062f\u0629 \u0648\u0627\u0644\u0644\u0637\u0641.<\/p>\n

\u0645\u0627 \u0645\u062f\u0649 \u0627\u0646\u062a\u0634\u0627\u0631 \u0623\u0645\u0631\u0627\u0636 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631 \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629\u061f<\/strong><\/span><\/h2>\n

\u0637\u0641\u0644 \u0648\u0627\u062d\u062f \u0645\u0646 \u0628\u064a\u0646 \u062e\u0645\u0633\u0629 \u0648\u0639\u0634\u0631\u064a\u0646 \u0623\u0644\u0641 \u0648\u0644\u0627\u062f\u0629 \u064a\u0635\u0627\u0628 \u0628\u0646\u0648\u0639 \u0645\u0646 \u0623\u0646\u0648\u0627\u0639 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631 \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629 \u0641\u064a \u0627\u0644\u0648\u0644\u0627\u064a\u0627\u062a \u0627\u0644\u0645\u062a\u062d\u062f\u0629.<\/p>\n

\u0637\u0631\u064a\u0642\u0629 \u062a\u0648\u0631\u064a\u062b \u0623\u0645\u0631\u0627\u0636 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631 \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629<\/span><\/h1>\n

\u0643\u0644 \u0623\u0646\u0648\u0627\u0639 \u0623\u0645\u0631\u0627\u0636 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631 \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629 \u0644\u0647\u0627 \u0637\u0631\u064a\u0642\u0629 \u0648\u0627\u062d\u062f\u0629 \u0641\u064a \u0627\u0646\u062a\u0642\u0627\u0644 \u0627\u0644\u0645\u0631\u0636 \u0645\u0646 \u0627\u0644\u0648\u0627\u0644\u062f\u064a\u0646 \u0625\u0644\u0649 \u0627\u0644\u0623\u0628\u0646\u0627\u0621 \u0639\u062f\u0627 \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u062b\u0627\u0646\u064a \u0645\u062a\u0644\u0627\u0632\u0645\u0629 \u0647\u0646\u062a\u0631) \u0641\u0647\u064a \u062a\u0646\u062a\u0642\u0644 \u0628\u0627\u0644\u0648\u0631\u0627\u062b\u0629 \u0627\u0644\u0645\u0631\u062a\u0628\u0637\u0629 \u0628\u0627\u0644\u062c\u0646\u0633 \u0641\u0644\u0627 \u062a\u0635\u064a\u0628 \u0627\u0644\u0627 \u0627\u0644\u0630\u0643\u0648\u0631 \u0641\u0642\u0637. \u0643\u0645\u0627 \u0647\u0648 \u0645\u0639\u0644\u0648\u0645 \u0643\u0644 \u0627\u0646\u0633\u0627\u0646 \u0644\u062f\u064a\u0647 \u0645\u0648\u0631\u062b\u0627\u062a\u00a0 (\u062c\u064a\u0646\u0627\u062a) \u0648\u0631\u062b\u0647\u0627 \u0645\u0646 \u0648\u0627\u0644\u062f\u064a\u0647 . \u0648\u0647\u0630\u0647 \u0627\u0644\u0645\u0648\u0631\u062b\u0627\u062a \u062a\u062d\u062f\u062f \u0627\u0644\u0635\u0641\u0627\u062a \u0627\u0644\u0648\u0631\u0627\u062b\u064a\u0629 \u0645\u062b\u0644 \u0627\u0644\u0637\u0648\u0644 \u0648\u0627\u0644\u0642\u0635\u0631 \u0648\u0627\u0644\u0644\u0648\u0646 \u0648\u063a\u064a\u0631\u0647\u0627. \u0628\u0639\u0636 \u0648\u0643\u0644 \u062c\u064a\u0646 \u064a\u0627\u062a\u064a \u0639\u0644\u0649 \u0634\u0643\u0644 \u0646\u0633\u062e\u062a\u064a\u0646 \u0648\u0627\u062d\u062f\u0647 \u0645\u0646 \u0627\u0644\u0627\u0628 \u0648 \u0627\u0644\u0627\u062e\u0631\u0649 \u0645\u0646 \u0627\u0644\u0627\u0645. \u0648\u0627\u0644\u062c\u064a\u0646\u0627\u062a \u0647\u064a \u0627\u0644\u062a\u064a \u062a\u0635\u0646\u0639 \u0627\u0644\u0627\u0646\u0632\u064a\u0645\u0627\u062a \u0641\u064a \u0627\u0644\u062c\u0633\u0645. \u0644\u0648\u062d\u062f\u062b \u062e\u0644\u0644 \u0641\u064a \u0627\u062d\u062f \u0627\u0644\u062c\u064a\u0646\u0627\u062a (\u0637\u0641\u0631\u0629) \u0641\u0627\u0646 \u0627\u0644\u062c\u0633\u0645 \u0641\u064a \u0627\u0644\u0639\u0627\u062f\u0629 \u0644\u0627 \u064a\u062a\u0636\u0631\u0631 \u0627\u0630\u0627 \u0643\u0627\u0646\u062a \u0627\u0644\u0646\u0633\u062e\u0629 \u0627\u0644\u0627\u062e\u0631\u0649 \u0633\u0644\u064a\u0645\u0629 .\u0644\u0643\u0646 \u0627\u0644\u0645\u0631\u0636 \u064a\u0638\u0647\u0631 \u0627\u0630\u0627 \u0643\u0627\u0646 \u0643\u0644\u0627 \u0627\u0644\u0646\u0633\u062e\u062a\u064a\u0646 \u0627\u0644\u062a\u064a \u0648\u0631\u062b\u0647\u0627 \u0627\u0644\u0627\u0646\u0633\u0627\u0646 \u0645\u0646 \u0648\u0627\u0644\u062f\u064a\u0647 \u0641\u064a\u0647\u0627 \u062e\u0644\u0644 \u0648 \u0644\u0630\u0644\u0643 \u062a\u0633\u0645\u0649 \u0647\u0630\u0647 \u0627\u0644\u0627\u0645\u0631\u0627\u0636 \u0627\u0645\u0631\u0627\u0636 \u0648\u0631\u0627\u062b\u064a\u0629 \u0645\u062a\u0646\u062d\u064a\u0629 \u0623\u064a \u0627\u0646 \u0627\u0644\u062c\u064a\u0646 \u0644\u0627 \u064a\u0638\u0647\u0631 \u0627\u0644\u0649 \u0627\u0630\u0627 \u0643\u0627\u0646 \u0643\u0644\u0627 \u0627\u0644\u0646\u0633\u062e\u062a\u064a\u0646 \u0645\u0639\u0637\u0648\u0628\u062a\u0627\u0646.<\/p>\n

\u0627\u0630\u0627 \u062a\u0632\u0648\u062c \u0634\u062e\u0635 \u064a\u062d\u0645\u0644 \u0627\u0644\u062c\u064a\u0646 \u0627\u0644\u0645\u0639\u0637\u0648\u0628 \u0645\u0646 \u0622\u062e\u0631 \u064a\u062d\u0645\u0644 \u0630\u0627\u062a \u0627\u0644\u062c\u064a\u0646 \u0641\u0625\u0646 \u0647\u0646\u0627\u0643 \u0627\u062d\u062a\u0645\u0627\u0644\u0627 \u0646\u0633\u0628\u062a\u0647 25% \u0628\u0623\u0646 \u064a\u0635\u0627\u0628 \u0627\u0644\u0645\u0648\u0644\u0648\u062f \u0628\u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636. \u0648\u0647\u0630\u0627 \u0627\u0644\u0627\u062d\u062a\u0645\u0627\u0644 \u064a\u062a\u062c\u062f\u062f \u0641\u064a \u0643\u0644 \u062d\u0627\u0644\u0629 \u062d\u0645\u0644 \u0623\u064a \u0644\u064a\u0633 \u0644\u0647 \u0639\u0644\u0627\u0642\u0629 \u0628\u0627\u0644\u0648\u0644\u0627\u062f\u0627\u062a \u0627\u0644\u0633\u0627\u0628\u0642\u0629 \u0623\u0648 \u0627\u0644\u0644\u0627\u062d\u0642\u0629 . \u0648\u0647\u0646\u0627\u0643 \u0627\u062d\u062a\u0645\u0627\u0644 \u0628\u0646\u0633\u0628\u0629 2 \u0645\u0646 \u0628\u064a\u0646 \u0643\u0644 3 \u0641\u0631\u0635 \u0628\u0623\u0646 \u064a\u0643\u0648\u0646 \u0625\u062e\u0648\u0629 \u0627\u0644\u0645\u0648\u0644\u0648\u062f \u0627\u0644\u0645\u0635\u0627\u0628 \u062d\u0627\u0645\u0644\u064a\u0646 \u0644\u0644\u0645\u0631\u0636\u00a0 \u0648\u0644\u064a\u0633\u0648\u0627 \u0645\u0635\u0627\u0628\u064a\u0646 .<\/p>\n

\u0627\u0644\u0627\u0645\u0631\u0627\u0636 \u0639\u062f\u064a\u062f\u0629 \u0627\u0644\u0633\u0643\u0631\u064a\u0627\u062a \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629 \u0646\u0627\u062f\u0631 \u062c\u062f\u0627 \u0648\u0627\u062d\u062a\u0645\u0627\u0644\u00a0 \u0623\u0646\u00a0 \u064a\u062a\u0632\u0648\u062c \u0634\u062e\u0635 \u062d\u0627\u0645\u0644 \u0645\u0646 \u0622\u062e\u0631 \u062d\u0627\u0645\u0644 \u0623\u064a\u0636\u0627 \u064a\u0639\u062f \u0627\u062d\u062a\u0645\u0627\u0644\u0627 \u0636\u0626\u064a\u0644\u0627 \u062c\u062f\u0627 \u0648\u064a\u0646\u0635\u062d \u0628\u0623\u0646 \u0644\u0627 \u064a\u062a\u0645 \u0632\u0648\u0627\u062c \u0628\u064a\u0646 \u0623\u0628\u0646\u0627\u0621 \u0639\u0645\u0648\u0645\u0629 \u0623\u0648 \u062e\u0624\u0648\u0644\u0629 \u0623\u0648 \u062d\u062a\u0649 \u0623\u0642\u0627\u0631\u0628 \u0642\u0631\u064a\u0628\u064a\u0646 \u062f\u0627\u062e\u0644 \u0623\u0633\u0631\u062a\u0647\u0645 \u0627\u0644\u062a\u064a \u0644\u0647\u0627 \u062a\u0623\u0631\u064a\u062e \u0628\u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636\u00a0 \u0627\u0644\u0627 \u0628\u0639\u062f \u0627\u0644\u0641\u062d\u0635 \u0627\u0644\u0648\u0631\u0627\u062b\u064a \u0639\u0646 \u0627\u0644\u0645\u0631\u0636 . \u0643\u0645\u0627 \u064a\u062c\u0628 \u0645\u0639\u0631\u0641\u0647 \u0623\u0646\u0647 \u0644\u0627 \u064a\u0634\u062a\u0631\u0637\u00a0 \u0648\u062c\u0648\u062f \u062a\u0627\u0631\u064a\u062e \u0644\u0644\u0645\u0631\u0636 \u0641\u064a \u0627\u0644\u0623\u0633\u0631\u0629 \u0644\u0625\u062b\u0628\u0627\u062a \u0625\u0635\u0627\u0628\u0629 \u0637\u0641\u0644\u0647\u0627.<\/p>\n

\u0645\u0639\u0631\u0641\u0629 \u0627\u0644\u0645\u0632\u064a\u062f \u0627\u0644\u062e\u0635\u0627\u0626\u0635 \u0627\u0644\u062c\u0633\u062f\u064a\u0629<\/span><\/h1>\n

\u0627\u0639\u0631\u0627\u0636 \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0623\u0648\u0644 \u0644\u0645\u0631\u0636 \u0639\u062f\u064a\u062f \u0627\u0644\u0633\u0643\u0631 \u0627\u0644\u0645\u062e\u0627\u0637\u064a<\/strong> MPS1 disease<\/strong><\/span><\/h2>\n

\u062a\u0623\u062e\u0631 \u0641\u064a \u0646\u0645\u0648 \u0627\u0644\u062c\u0633\u062f\u064a \u0631\u063a\u0645 \u0623\u0646 \u0627\u0644\u0646\u0645\u0648 \u064a\u0643\u0648\u0646 \u0641\u064a \u0627\u0644\u0639\u0627\u062f\u0629 \u0637\u0628\u064a\u0639\u064a\u0627 \u0641\u064a \u0627\u0644\u0639\u0627\u0645 \u0627\u0644\u0623\u0648\u0644 \u0645\u0646 \u0639\u0645\u0631 \u0627\u0644\u0637\u0641\u0644.<\/p>\n

\u062a\u0623\u062e\u0631 \u0639\u0642\u0644\u064a \u064a\u062a\u0641\u0627\u0642\u0645 \u0645\u0639 \u0627\u0644\u0648\u0642\u062a<\/p>\n

\u063a\u0644\u0627\u0638\u0629 \u0641\u064a \u0645\u0644\u0627\u0645\u062d \u0627\u0644\u0648\u062c\u0647 \u0645\u0639 \u0627\u0644\u0648\u0642\u062a<\/p>\n

\u0639\u0627\u062a\u0645\u0647 \u0641\u064a \u0627\u0644\u0642\u0631\u0646\u064a\u0629<\/p>\n

\u0636\u0639\u0641 \u0641\u064a \u0627\u0644\u0633\u0645\u0639 \u0648 \u0635\u0645\u0645 \u0648 \u062a\u0643\u0631\u0627\u0631 \u0627\u0644\u062a\u0647\u0627\u0628 \u0627\u0644\u0627\u0630\u0646\u064a\u0646<\/p>\n

\u062a\u064a\u0628\u0633 \u0627\u0644\u0645\u0641\u0627\u0635\u0644<\/p>\n

\u0645\u0634\u0627\u0643\u0644 \u0641\u064a \u0635\u0645\u0627\u0645\u0627\u062a \u0627\u0644\u0642\u0644\u0628<\/p>\n

\u062a\u0634\u0648\u0647\u0627\u062a \u0641\u064a \u0627\u0644\u0642\u0641\u0635 \u0627\u0644\u0635\u062f\u0631\u064a<\/p>\n

\u0627\u0644\u062c\u0646\u0641 ( \u062a\u062d\u062f\u0628 \u0623\u0648 \u062a\u0642\u0648\u0633 \u0648 \u0645\u064a\u0644\u0627\u0646 \u0641\u064a \u0627\u0644\u0639\u0645\u0648\u062f \u0627\u0644\u0641\u0642\u0631\u064a)<\/p>\n

\u0628\u0631\u0648\u0632 \u0627\u0648 \u062f\u062e\u0648\u0644 \u0641\u064a \u0639\u0638\u0645\u0629 \u0627\u0644\u0642\u0635 \u0628\u0627\u0644\u0635\u062f\u0631<\/p>\n

\u0623\u0635\u0627\u0628\u0639 \u0627\u0644\u064a\u062f \u0644\u0647\u0627 \u0634\u0643\u0644 \u0645\u062e\u0644\u0628\u064a<\/p>\n

\u062a\u0634\u0648\u0647\u00a0 \u0627\u0644\u0623\u0633\u0646\u0627\u0646<\/p>\n

\u0642\u0635\u0631 \u0627\u0644\u0642\u0627\u0645\u0629<\/p>\n

\u0643\u0628\u0631 \u062d\u062c\u0645 \u0627\u0644\u0631\u0623\u0633<\/p>\n

\u062a\u0636\u062e\u0645 \u0627\u0644\u0643\u0628\u062f \u0648\u0627\u0644\u0637\u062d\u0627\u0644<\/p>\n

\u0634\u0641\u0627\u0647 \u0645\u0645\u062a\u0644\u0626\u0629<\/p>\n

\u0641\u062a\u0627\u0642 \u0627\u0644\u0633\u0631\u0629<\/p>\n

\u0628\u0631\u0648\u0632 \u0628\u0627\u0644\u062c\u0628\u0647\u0629<\/p>\n

\u062a\u0636\u062e\u0645 \u0641\u064a \u0627\u0644\u0644\u0633\u0627\u0646<\/p>\n

\u0627\u0639\u0631\u0627\u0636 \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u062b\u0627\u0646\u064a \u0644\u0645\u0631\u0636 \u0639\u062f\u064a\u062f \u0627\u0644\u0633\u0643\u0631 \u0627\u0644\u0645\u062e\u0627\u0637\u064a<\/strong> \u00a0(\u0647\u0646\u062a\u0631)<\/strong><\/span><\/h2>\n
    \n
  • \u064a\u0624\u062b\u0631 \u0639\u0644\u0649 \u0627\u0644\u0630\u0643\u0648\u0631 \u0648 \u0627\u0644\u0625\u0646\u0627\u062b \u064a\u0643\u0646 \u062d\u0627\u0645\u0644\u064a\u0647\u0627 \u060c \u0648\u0644\u0643\u0646 \u0646\u0627\u062f\u0631\u0627 \u0645\u0627 \u062a\u062a\u0623\u062b\u0631 \u0627\u0644\u0623\u0646\u062b\u0649.<\/li>\n
  • \u064a\u062e\u062a\u0644\u0641 \u0645\u0646 \u0634\u062f\u064a\u062f \u0625\u0644\u0649 \u0636\u0639\u064a\u0641<\/li>\n
  • \u062a\u0634\u0628\u0647 \u0627\u0644\u0623\u0639\u0631\u0627\u0636 \u0627\u0644\u062e\u0627\u0631\u062c\u064a\u0629 \u0645\u0644\u0627\u0645\u062d \u0627\u0644\u0627\u0634\u062e\u0627\u0635 \u0645\u0646 \u0630\u0648\u064a \u0645\u062a\u0644\u0627\u0632\u0645\u0629 \u0647\u064a\u0631\u0644\u0631 (MPS Type 1)<\/li>\n
  • \u0642\u062f \u062a\u062a\u0623\u062b\u0631 \u0627\u0644\u0642\u062f\u0631\u0627\u062a \u0627\u0644\u0639\u0642\u0644\u064a\u0629 \u0628\u064a\u0646 \u062a\u0627\u062b\u0631 \u0634\u062f\u064a\u062f \u0627\u0644\u0649 \u062e\u0641\u064a\u0641<\/li>\n<\/ul>\n

    \u0627\u0639\u0631\u0627\u0636 \u0627\u0644\u0646\u0648\u0639 \u0627\u0644\u0631\u0627\u0628\u0639 \u0644\u0645\u0631\u0636 \u0639\u062f\u064a\u062f \u0627\u0644\u0633\u0643\u0631 \u0627\u0644\u0645\u062e\u0627\u0637\u064a<\/strong> (\u0645\u0648\u0643\u064a\u0648) <\/strong><\/p>\n

      \n
    • \u063a\u0644\u0627\u0638\u0629 \u0641\u064a \u0645\u0644\u0627\u0645\u062d \u0627\u0644\u0648\u062c\u0647<\/li>\n
    • \u062a\u0634\u0648\u0647\u0627\u062a \u0627\u0644\u0647\u064a\u0643\u0644 \u0627\u0644\u0639\u0638\u0645\u064a<\/li>\n
    • \u0645\u062a\u0644\u0627\u0632\u0645\u0629 \u0627\u0644\u0646\u0641\u0642 \u0627\u0644\u0631\u0633\u063a\u064a<\/li>\n
    • \u062a\u064a\u0628\u0633 \u0627\u0644\u0645\u0641\u0627\u0635\u0644<\/li>\n
    • \u0627\u0644\u0645\u0634\u064a \u063a\u064a\u0631 \u0637\u0628\u064a\u0639\u064a<\/li>\n
    • \u0645\u0634\u0627\u0643\u0644 \u0641\u064a \u0627\u0644\u062a\u0646\u0641\u0633<\/li>\n
    • \u0645\u0634\u0627\u0643\u0644 \u0627\u0644\u0639\u064a\u0646<\/li>\n
    • \u0636\u0639\u0641 \u0627\u0644\u0633\u0645\u0639<\/li>\n
    • \u0645\u0634\u0627\u0643\u0644 \u0627\u0644\u0623\u0633\u0646\u0627\u0646<\/li>\n
    • \u062a\u0636\u062e\u0645 \u0627\u0644\u0643\u0628\u062f \u0648\u0627\u0644\u0637\u062d\u0627\u0644 \u0641\u064a \u0628\u0639\u0636 \u0627\u0644\u062d\u0627\u0644\u0627\u062a<\/li>\n
    • \u0627\u0644\u062c\u0646\u0641 \u062a\u062d\u062f\u062b \u0645\u0628\u0643\u0631\u0627\u064b \u0648\u0628\u0634\u0643\u0644 \u062d\u0627\u062f<\/li>\n
    • \u062a\u0631\u0627\u062c\u0639 \u0627\u0644\u0642\u062f\u0631\u0627\u062a \u0627\u0644\u0639\u0642\u0644\u064a\u0629<\/li>\n
    • \u0644\u0627 \u064a\u0624\u062b\u0631 \u0639\u0644\u0649 \u0627\u0644\u0639\u0642\u0644 \u0641\u064a \u0627\u0644\u0639\u0627\u062f\u0629 \u0648 \u0642\u062f \u062a\u062a\u0623\u062e\u0631 \u0644\u0627\u062d\u0642\u0627\u064b<\/li>\n
    • \u0627\u0644\u0633\u0644\u0648\u0643 \u0627\u0644\u0639\u062f\u0648\u0627\u0646\u064a \u0648\u0641\u0631\u0637 \u0627\u0644\u0646\u0634\u0627\u0637<\/li>\n
    • \u0627\u0644\u0635\u0631\u0639<\/li>\n<\/ul>\n

      \u0644\u064a\u0633 \u0628\u0627\u0644\u0636\u0631\u0648\u0631\u0629 \u0623\u0646 \u062a\u0646\u0637\u0628\u0642 \u0643\u0644 \u0647\u0630\u0647 \u0627\u0644\u0639\u0644\u0627\u0645\u0627\u062a \u0639\u0644\u0649 \u0627\u0644\u0645\u0631\u064a\u0636 \u0645\u0639 \u0645\u0644\u0627\u062d\u0638\u0629 \u0623\u0646 \u0645\u0639\u0638\u0645\u0647\u0627 \u0645\u0634\u062a\u0631\u0643 \u0628\u064a\u0646 \u0645\u0639\u0638\u0645 \u0623\u0645\u0631\u0627\u0636 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631 \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629<\/p>\n

      \u0627\u0644\u0641\u062d\u0648\u0635\u0627\u062a \u0627\u0644\u0637\u0628\u064a\u0629 \u0641\u064a<\/strong>\u00a0\u00a0 mps1<\/strong><\/span><\/h2>\n

      \u0641\u064a \u0627\u0644\u0628\u062f\u0627\u064a\u0629 \u0639\u0627\u062f\u0629 \u064a\u062c\u0631\u0649 \u0641\u062d\u0635 \u0627\u0644\u0628\u0648\u0644 \u0644\u0642\u064a\u0627\u0633 . \u0627\u0644\u0645\u0648\u0627\u062f \u0627\u0644\u0633\u0643\u0631\u064a\u0629 \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629\u00a0 \u0648 \u0627\u0644\u062a\u064a \u062a\u0633\u0627\u0639\u062f \u0643\u062b\u064a\u0631\u0627\u064b \u0641\u064a \u0627\u0644\u062a\u0634\u062e\u064a\u0635 \u0639\u0646\u062f \u0627\u0644\u0627\u0634\u062a\u0628\u0627\u0647 \u0628\u0647\u0627. \u0644\u0643\u0646 \u0641\u062d\u0635 \u0627\u0644\u0628\u0648\u0644 \u0644\u0627 \u064a\u0648\u0636\u062d \u0646\u0648\u0639 \u0627\u0644\u0645\u0631\u0636 \u0645\u0646 \u0628\u064a\u0646 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631 \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629. \u0648\u0644\u062a\u062d\u062f\u064a\u062f \u0627\u0644\u0646\u0648\u0639 \u064a\u062c\u0628 \u0625\u062c\u0631\u0627\u0621 \u0641\u062d\u0635 \u0646\u0634\u0627\u0637 \u0627\u0644\u0625\u0646\u0632\u064a\u0645 \u0641\u064a \u0627\u0644\u062f\u0645 \u0623\u0648 \u0628\u0623\u062e\u0630 \u0639\u064a\u0646\u0629 \u0645\u0646 \u0627\u0644\u062c\u0644\u062f. \u0648\u0627\u0644\u0627\u0646\u0632\u064a\u0645 \u0627\u0644\u0630\u064a \u064a\u062c\u0628 \u0641\u062d\u0635\u0647 \u0641\u064a \u0647\u0630\u0647 \u0627\u0644\u062d\u0627\u0644\u0629 \u064a\u0633\u0645\u0649\u00a0 alpha-L-iduronidase .\u0623\u064a\u0636\u0627 \u064a\u0645\u0643\u0646 \u0623\u062e\u0630 \u0635\u0648\u0631 \u0623\u0634\u0639\u0629\u00a0 \u0644\u0644\u0639\u0645\u0648\u062f \u0627\u0644\u0641\u0642\u0631\u064a \u0648 \u062a\u062e\u0637\u064a\u0637 \u0644\u0644\u0642\u0644\u0628 \u0644\u0645\u0639\u0631\u0641\u0629 \u0648\u0638\u064a\u0641\u0629 \u0627\u0644\u0642\u0644\u0628 \u0648 \u0627\u0644\u0627\u0637\u0645\u0626\u0646\u0627\u0646 \u0639\u0644\u0649 \u0627\u0644\u0635\u0645\u0627\u0645\u0627\u062a .<\/p>\n

      \u0627\u0644\u0639\u0644\u0627\u062c<\/strong>:<\/strong><\/span><\/h1>\n

      1- \u062d\u062f\u064a\u062b\u0627 \u062a\u0645\u0643\u0646\u062a \u0628\u0639\u0636 \u0627\u0644\u0645\u0624\u0633\u0633\u0627\u062a \u0627\u0644\u0637\u0628\u064a\u0629 \u0645\u0646 \u0625\u0646\u062a\u0627\u062c \u0627\u0644\u0625\u0646\u0632\u064a\u0645 \u0627\u0644\u0645\u0641\u0642\u0648\u062f \u0648\u0627\u0644\u0630\u064a \u064a\u0645\u062b\u0644 \u063a\u064a\u0627\u0628\u0647 \u0623\u0635\u0644 \u0627\u0644\u0645\u0634\u0643\u0644\u0629 \u0648\u0647\u0648 \u064a\u062d\u0642\u0646 \u0641\u064a \u0627\u0644\u062f\u0645 \u0628\u0635\u0648\u0631\u0629 \u0645\u062a\u0643\u0631\u0631\u0629 .<\/p>\n

      2- \u0632\u0631\u0627\u0639\u0629 \u0646\u062e\u0627\u0639 \u0627\u0644\u0639\u0638\u0645 \u0623\u0648 \u0627\u0644\u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u062c\u0630\u0639\u064a\u0629 \u0627\u0644\u0645\u0633\u062a\u062e\u0631\u062c\u0629 \u0645\u0646 \u062f\u0645 \u0627\u0644\u062d\u0628\u0644 \u0627\u0644\u0633\u0631\u064a \u0645\u0646 \u0645\u062a\u0628\u0631\u0639 \u0645\u0637\u0627\u0628\u0642 \u0628\u062f\u0631\u062c\u0629 \u0643\u0628\u064a\u0631\u0629 \u0647\u0630\u0627 \u0627\u0644\u0639\u0644\u0627\u062c \u0623\u062b\u0628\u062a \u0641\u0627\u0626\u062f\u0629 \u0644\u0644\u0639\u062f\u064a\u062f \u0645\u0646 \u0627\u0644\u062d\u0627\u0644\u0627\u062a \u0641\u0627\u0633\u062a\u0637\u0627\u0639\u0648\u0627 \u0625\u0646\u062a\u0627\u062c \u0627\u0644\u0625\u0646\u0632\u064a\u0645 \u0628\u062e\u0644\u0627\u064a\u0627\u0647\u0645 \u0627\u0644\u062c\u062f\u064a\u062f\u0629 \u0648\u0644\u0643\u0646 \u0627\u0644\u0639\u0645\u0644\u064a\u0629 \u0644\u0647\u0627 \u0645\u062e\u0627\u0631\u0637\u0647\u0627 \u0648\u062a\u0639\u0642\u064a\u062f\u0627\u062a\u0647\u0627. \u0648\u0641\u064a \u0647\u0630\u0647 \u0627\u0644\u062d\u0627\u0644\u0629 \u064a\u062c\u0628 \u0625\u062c\u0631\u0627\u0621 \u0627\u0644\u0639\u0645\u0644\u064a\u0629\u00a0 \u0645\u0628\u0643\u0631\u0627 \u0642\u0628\u0644 \u062d\u062f\u0648\u062b \u0623\u0636\u0631\u0627\u0631 \u0641\u064a \u062e\u0644\u0627\u064a\u0627 \u0627\u0644\u0645\u062e<\/p>\n

      3- \u0647\u0646\u0627\u0643 \u0645\u062d\u0627\u0648\u0644\u0627\u062a \u0644\u0645\u0627 \u064a\u0633\u0645\u0649 \u0627\u0644\u0639\u0644\u0627\u062c \u0627\u0644\u062c\u064a\u0646\u064a \u0623\u0648 \u0627\u0635\u0644\u0627\u062d \u0627\u0644\u062c\u064a\u0646 \u0627\u0644\u0645\u0639\u0637\u0648\u0628 \u0628\u062a\u0642\u0646\u064a\u0629 \u0643\u0631\u064a\u0633\u0628\u0631 \u0648\u0647\u064a \u0641\u064a \u0637\u0648\u0631 \u0627\u0644\u062f\u0631\u0627\u0633\u0629<\/p>\n

      4- \u0623\u0639\u0636\u0627\u0621 \u0627\u0644\u062c\u0633\u0645 \u0627\u0644\u0645\u062a\u0623\u062b\u0631\u0629 \u0628\u0627\u0644\u0645\u0631\u0636 \u0643\u0627\u0644\u0642\u0644\u0628 \u0645\u062b\u0644\u0627\u00a0 \u064a\u0645\u0643\u0646 \u0627\u0644\u062a\u0639\u0627\u0645\u0644 \u0645\u0639\u0647\u0627 \u0628\u0627\u0644\u0637\u0631\u0642 \u0627\u0644\u0637\u0628\u064a\u0629 \u0627\u0644\u0627\u0639\u062a\u064a\u0627\u062f\u064a\u0629 \u0643\u0645\u0627 \u064a\u0645\u0643\u0646 \u0632\u0631\u0627\u0639\u0629 \u0642\u0631\u0646\u064a\u0629 \u0627\u0644\u0639\u064a\u0646\u00a0 \u0643\u0645\u0627 \u064a\u0645\u0643\u0646 \u0632\u0631\u0627\u0639\u0629 \u0642\u0631\u0646\u064a\u0629 \u0627\u0644\u0639\u064a\u0646 \u0630\u0627 \u0644\u0632\u0645 \u0627\u0644\u0623\u0645\u0631<\/p>\n

      5- \u064a\u062c\u0628 \u0627\u0644\u0627\u0647\u062a\u0645\u0627\u0645 \u0628\u0627\u0644\u0639\u0644\u0627\u062c \u0627\u0644\u0637\u0628\u064a\u0639\u064a \u0648 \u0627\u0644\u0648\u0638\u064a\u0641\u064a \u0648 \u0627\u0644\u0646\u0637\u0642 \u0648 \u062a\u0646\u0645\u064a\u0629 \u0627\u0644\u0645\u0647\u0627\u0631\u062a<\/p>\n

      \u0627\u062c\u0647\u0632\u0629 \u0645\u0633\u0627\u0639\u062f\u0629 \u0644\u0644\u0633\u0645\u0639<\/p>\n

      \u0639\u0644\u0627\u062c \u0645\u0634\u0627\u0643\u0644 \u0627\u0644\u0631\u0633\u063a \u0637\u0628\u064a\u0627\u064b \u0623\u0648 \u062c\u0631\u0627\u062d\u064a\u0627<\/p>\n

      \u0639\u0644\u0627\u062c \u0645\u0634\u0627\u0643\u0644 \u0627\u0644\u062c\u0647\u0627\u0632 \u0627\u0644\u0647\u0636\u0645\u064a \u0648 \u0627\u0644\u0627\u0645\u0633\u0627\u0643<\/p>\n

      \u0627\u062d\u062a\u064a\u0627\u062c\u0627\u062a \u0627\u0644\u0637\u0628\u064a\u0629 \u0648 \u0627\u0644\u063a\u0630\u0627\u0626\u064a\u0629<\/span><\/h1>\n

      \u0645\u0627 \u062a\u062d\u062a\u0627\u062c \u0625\u0644\u0649 \u0645\u0639\u0631\u0641\u062a\u0647<\/strong><\/span><\/h1>\n

      \u0627\u0644\u062a\u063a\u064a\u064a\u0631 \u0641\u064a \u0627\u0644\u0646\u0645\u0637 \u00a0\u0627\u0644\u063a\u0630\u0627\u0626\u064a \u0644\u0627 \u062a\u0641\u064a\u062f \u0641\u064a \u0639\u0644\u0627\u062c \u00a0\u0648\u0644\u0630\u0644\u0643 \u064a\u0646\u0635\u062d \u0628\u0646\u0645\u0637 \u063a\u0630\u0627\u0626\u064a \u0645\u062a\u0648\u0627\u0632\u0646.<\/p>\n

      \u0625\u0630\u0627 \u0643\u0627\u0646 \u0627\u0644\u0637\u0641\u0644 \u064a\u0639\u0627\u0646\u064a \u0645\u0646 \u0627\u0646\u0642\u0637\u0627\u0639 \u0627\u0644\u0646\u0641\u0633 \u0623\u062b\u0646\u0627\u0621 \u0627\u0644\u0646\u0648\u0645 \u0623\u0648 \u0627\u0636\u0637\u0631\u0627\u0628 \u0641\u064a \u0645\u062c\u0631\u0649 \u0627\u0644\u0647\u0648\u0627\u0621 \u0628\u0633\u0628\u0628 \u062a\u0636\u064a\u0642 \u0645\u062c\u0631\u0649 \u0627\u0644\u062a\u0646\u0641\u0633 \u0628\u0633\u0628\u0628 \u062a\u0636\u062e\u0645 \u0627\u0644\u0644\u062d\u0645\u064a\u0627\u062a \u062e\u0644\u0641 \u0627\u0644\u0623\u0646\u0641 \u0623\u0648 \u0627\u0644\u0644\u0648\u0632 \u0641\u064a\u0645\u0643\u0646 \u0625\u062c\u0631\u0627\u0621 \u0639\u0645\u0644\u064a\u0629 \u062c\u0631\u0627\u062d\u064a\u0629 \u0644\u0625\u0632\u0627\u0644\u0629 \u0627\u0644\u0644\u0648\u0632\u062a\u064a\u0646 \u0627\u0644\u0632\u0648\u0627\u0626\u062f \u0627\u0644\u0644\u062d\u0645\u064a\u0629 \u0644\u062a\u062d\u0633\u064a\u0646 \u0627\u0644\u062a\u0646\u0641\u0633. \u0643\u0645\u0627 \u0623\u0646 \u0639\u0645\u0644 \u062f\u0631\u0627\u0633\u0629 \u0644\u0644\u0646\u0648\u0645 \u0644\u062a\u0642\u064a\u064a\u0645 \u062d\u0627\u0644\u0629 \u0645\u062c\u0631\u0649 \u0627\u0644\u0647\u0648\u0627\u0621 \u0648\u0627\u0644\u062d\u0627\u062c\u0629 \u0644\u0644\u0623\u0643\u0633\u062c\u064a\u0646 \u0639\u0646\u062f \u0627\u0644\u0646\u0648\u0645.<\/p>\n

      \u0648\u064a\u0645\u0643\u0646 \u0623\u064a\u0636\u0627 \u0625\u062c\u0631\u0627\u0621 \u062c\u0631\u0627\u062d\u0629 \u0644\u062a\u0635\u062d\u064a\u062d \u0627\u0644\u0641\u062a\u0642 \u0627\u0630\u0627 \u0648\u062c\u062f\u060c \u0623\u0648 \u0627\u062c\u0631\u0627\u0621 \u0639\u0645\u0644\u064a\u0629 \u0644\u0644\u0645\u0633\u0627\u0639\u062f\u0629 \u0641\u064a \u062a\u0635\u0631\u064a\u0641 \u0627\u0644\u0633\u0627\u0626\u0644 \u0627\u0644\u0633\u062d\u0627\u0626\u064a \u0627\u0630\u0627 \u0643\u0627\u0646 \u0647\u0646\u0627\u0643 \u0636\u063a\u0637 \u0639\u0644\u0649 \u0627\u0644\u062f\u0645\u0627\u063a. \u0623\u0648 \u0644\u062a\u062e\u0641\u064a\u0641 \u0627\u0644\u0636\u063a\u0637 \u0639\u0644\u0649 \u0627\u0644\u0623\u0639\u0635\u0627\u0628 \u0641\u064a \u0627\u0644\u062d\u0628\u0644 \u0627\u0644\u0634\u0648\u0643\u064a \u0628\u0633\u0628\u0628 \u0636\u063a\u0637 \u0627\u0644\u0647\u064a\u0643\u0644 \u0627\u0644\u0639\u0638\u0645\u064a \u0648\u063a\u064a\u0631 \u0630\u0644\u0643 \u0645\u0646 \u0627\u0644\u062a\u0634\u0648\u0647\u0627\u062a.<\/p>\n

      \u0645\u0634\u0627\u0643\u0644 \u0627\u0644\u062d\u0631\u0643\u0629 \u060c \u0648\u0641\u0642\u062f\u0627\u0646 \u0627\u0644\u0633\u0645\u0639 \u0648\u0635\u0639\u0648\u0628\u0629 \u0627\u0644\u0631\u0624\u064a\u0629 \u0647\u064a \u0645\u0646 \u0627\u0644\u0645\u0636\u0627\u0639\u0641\u0627\u062a \u0627\u0644\u0637\u0628\u064a\u0629 \u0627\u0644\u0631\u0626\u064a\u0633\u064a\u0629 \u0644\u0627\u0645\u0631\u0627\u0636 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631\u064a\u0627\u062a \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629 \u0627\u0644\u062a\u064a \u0642\u062f \u062a\u062d\u062a\u0627\u062c \u0625\u0644\u0649 \u0627\u0647\u062a\u0645\u0627\u0645 \u062e\u0627\u0635 \u0645\u0646 \u0627\u062f\u0627\u0631\u0629 \u00a0\u0627\u0644\u0645\u062f\u0631\u0633\u0629 \u0648 \u0627\u0644\u0645\u062f\u0631\u0633\u064a\u0646 \u0641\u064a \u00a0\u062a\u062e\u0637\u064a\u0637 \u0627\u0644\u0628\u0631\u0646\u0627\u0645\u062c \u0627\u0644\u0645\u0646\u0627\u0633\u0628 \u0644\u0644\u0637\u0627\u0644\u0628. \u0645\u0646 \u0627\u0644\u0645\u0647\u0645 \u0645\u0646\u0627\u0642\u0634\u0629 \u0637\u0628\u064a\u0639\u0629 \u062d\u0627\u0644\u0629 \u0627\u0644\u0637\u0627\u0644\u0628 \u0648\u062a\u0623\u062b\u064a\u0631\u0627\u062a\u0647\u0627 \u0639\u0644\u0649 \u0627\u0644\u0623\u0646\u0634\u0637\u0629 \u0627\u0644\u0645\u062f\u0631\u0633\u064a\u0629. \u0633\u064a\u062d\u062f\u062f \u0623\u0637\u0628\u0627\u0621 \u0645\u0633\u062a\u0648\u064a\u0627\u062a \u0627\u0644\u0646\u0634\u0627\u0637 \u0627\u0644\u0645\u0633\u0645\u0648\u062d \u0628\u0647\u0627 \u0644\u0644\u0637\u0627\u0644\u0628 \u0627\u0630\u0627 \u0643\u0627\u0646 \u0647\u0646\u0627\u0643 \u0623\u064a \u062a\u0623\u062b\u064a\u0631 \u0639\u0644\u0649 \u0635\u062d\u062a\u0647.<\/p>\n

      \u0642\u062f \u064a\u0643\u0648\u0646 \u0644\u062f\u0649 \u0627\u0644\u0623\u0637\u0641\u0627\u0644 \u0641\u064a \u0633\u0646 \u0627\u0644\u0645\u062f\u0631\u0633\u0629 \u0627\u0644\u0639\u062f\u064a\u062f \u0645\u0646 \u0627\u0644\u0645\u062e\u062a\u0635\u064a\u0646 \u0627\u0644\u0630\u064a\u0646 \u064a\u062a\u0627\u0628\u0639\u0648\u0646 \u062d\u0627\u0644\u0629 \u0627\u0644\u0637\u0641\u0644 \u0641\u064a \u0627\u0644\u0645\u0633\u062a\u0634\u0641\u0649 \u0645\u0646 \u0627\u0637\u0628\u0627\u0621 \u0627\u0644\u0623\u0637\u0641\u0627\u0644 \u0627\u0644\u0639\u0627\u0645\u064a\u064a\u0646 \u0627\u0644\u0649 \u0627\u0637\u0628\u0627\u0621 \u0627\u0644\u0623\u0645\u0631\u0627\u0636 \u0627\u0644\u0648\u0631\u0627\u062b\u064a\u0629 \u0648 \u062c\u0631\u0627\u062d\u0629 \u0627\u0644\u0623\u0646\u0641 \u0648\u0627\u0644\u0627\u0630\u0646 \u0648 \u0627\u0644\u062d\u0646\u062c\u0631\u0629 \u0648 \u0627\u0644\u0645\u062e \u0648\u0627\u0644\u0627\u0639\u0635\u0627\u0628 \u0648 \u0627\u0644\u0646\u0645\u0648 \u0648 \u063a\u064a\u0631\u0647\u0627.<\/p>\n

      \u0645\u0627 \u062a\u0633\u062a\u0637\u064a\u0639 \u0641\u0639\u0644\u0647<\/strong><\/span><\/h1>\n
        \n
      • \u064a\u062c\u0628 \u0625\u062c\u0631\u0627\u0621 \u0641\u062d\u0635 \u0633\u0646\u0648\u064a \u0648 \u062a\u0642\u064a\u064a\u0645 \u062f\u0648\u0631\u064a \u062d\u0633\u0628 \u0627\u0644\u062d\u0627\u062c\u0629 \u0644\u0644\u0637\u0641\u0644.<\/li>\n
      • \u0643\u0646 \u0639\u0644\u0649 \u062f\u0631\u0627\u064a\u0629 \u0628\u0623\u064a \u062a\u063a\u064a\u0631\u0627\u062a \u0641\u064a \u0627\u0644\u0633\u0644\u0648\u0643 \u0623\u0648 \u0627\u0644\u0645\u0632\u0627\u062c \u062a\u0628\u062f\u0648 \u063a\u064a\u0631 \u0639\u0627\u062f\u064a\u0629 \u0648 \u0627\u062e\u0628\u0631 \u0627\u0644\u0648\u0627\u0644\u062f\u064a\u0646 \u0639\u0646\u0647\u0627.<\/li>\n
      • \u0643\u0646 \u0639\u0644\u0649 \u062f\u0631\u0627\u064a\u0629 \u0628\u0627\u0644\u062a\u063a\u064a\u0631\u0627\u062a \u0641\u064a \u0627\u0644\u0631\u0624\u064a\u0629 \u062d\u064a\u062b \u0623\u0646 \u0639\u0627\u062a\u0645\u0629 \u0627\u0644\u0642\u0631\u0646\u064a\u0629 \u064a\u0645\u0643\u0646 \u0623\u0646 \u062a\u062a\u0637\u0648\u0631 \u0645\u0639 \u0627\u0644\u0648\u0642\u062a.\u064b<\/li>\n
      • \u0644\u0627\u062d\u0638 \u0623\u064a \u0646\u0639\u0627\u0633 \u0645\u0641\u0631\u0637 \u062e\u0644\u0627\u0644 \u0627\u0644\u0646\u0647\u0627\u0631 \u0644\u0644\u0637\u0627\u0644\u0628 \u0623\u0648 \u0646\u0648\u0645 \u062e\u0644\u0627\u0644 \u0627\u0644\u0638\u0647\u0631 \u0641\u064a \u0627\u0644\u0645\u062f\u0631\u0633\u0629 \u060c \u0648\u0625\u0628\u0644\u0627\u063a \u0627\u0644\u0648\u0627\u0644\u062f\u064a\u0646 \u0639\u0646 \u0623\u064a \u0645\u0644\u0627\u062d\u0638\u0629 \u0645\u062b\u0644 \u0627\u0644\u0634\u062e\u064a\u0631.<\/li>\n
      • \u0643\u0646 \u0639\u0644\u0649 \u062f\u0631\u0627\u064a\u0629 \u0628\u0623\u064a \u062a\u064a\u0628\u0633 \u0641\u064a \u0627\u0644\u0645\u0641\u0627\u0635\u0644 \u0642\u062f \u064a\u062c\u0639\u0644 \u062d\u0644 \u0627\u0644\u0648\u0627\u062c\u0628\u0627\u062a \u0627\u0644\u062f\u0631\u0627\u0633\u064a\u0629 \u0623\u0643\u062b\u0631 \u0635\u0639\u0648\u0628\u0629.<\/li>\n
      • \u0645\u0646 \u0627\u0644\u0645\u0647\u0645 \u0623\u0646 \u062a\u0643\u0648\u0646 \u0639\u0644\u0649 \u062f\u0631\u0627\u064a\u0629 \u0628\u0623\u064a \u062a\u063a\u064a\u064a\u0631\u0627\u062a \u0623\u0643\u0627\u062f\u064a\u0645\u064a\u0629. \u0641\u0642\u0645 \u0628\u0627\u0644\u0627\u0627\u062a\u0635\u0644 \u0628\u0627\u0644\u0648\u0627\u0644\u062f\u064a\u0646 \u0639\u0646\u062f \u0645\u0644\u0627\u062d\u0638\u0629 \u0623\u064a \u0627\u062e\u062a\u0644\u0627\u0641 \u0648\u062a\u063a\u064a\u0631.<\/li>\n<\/ul>\n

        \u064a\u062c\u0628 \u0648\u0636\u0639 \u062e\u0637\u0629 \u0627\u0644\u0637\u0648\u0627\u0631\u0626 \u0627\u0644\u062e\u0627\u0635\u0629 \u0639\u0646\u062f \u062d\u062f\u0648\u062b \u0646\u0648\u0628\u0627\u062a \u0635\u0631\u0639 \u0627\u0630\u0627 \u0643\u0627\u0646 \u0627\u0644\u0637\u0641\u0644 \u064a\u0639\u0627\u0646\u064a \u0645\u0646 \u0627\u0644\u0635\u0631\u0639.<\/p>\n

          \n
        • \u0642\u062f \u064a\u062d\u062a\u0627\u062c \u0627\u0644\u0637\u0644\u0627\u0628 \u0625\u0644\u0649 \u0632\u064a\u0627\u0631\u0629 \u063a\u0631\u0641\u0629 \u0627\u0644\u062a\u0645\u0631\u064a\u0636 \u0641\u064a \u0627\u0644\u0645\u062f\u0631\u0633\u0629 \u0627\u0630\u0627 \u0643\u0627\u0646\u062a \u0645\u062a\u0648\u0641\u0631\u0629 \u0644\u062a\u0646\u0627\u0648\u0644 \u0627\u0644\u0623\u062f\u0648\u064a\u0629 \u0623\u062b\u0646\u0627\u0621 \u0627\u0644\u062f\u0631\u0627\u0633\u0629.<\/li>\n
        • \u0625\u0630\u0627 \u0622\ufe8e\ufee7\ufe96 \u0647\u0646\u0627\u0643 \u0645\u0634\u0627\u0643\u0644 \ufed3\ufef2 \u0627\ufedf\ufed8\ufee0\ufe90 \u0642\u062f \u064a\u062d\u062a\u0627\u062c \u0627\u0644\u0645\u0639\u0644\u0645\u0648\u0646 \u0627\u0644\u062a\u062f\u0631\u064a\u0628\u0627\u062a \u0627\u0644\u0635\u062d\u064a\u0629 \u0627\u0644\u0627\u0632\u0645\u0629 \u0644\u0645\u062b\u0644 \u0647\u0630\u0647 \u0627\u0644\u062d\u0627\u0644\u0627\u062a \u0645\u062b\u0644 \u0627\u0644\u0627\u0646\u0639\u0627\u0634 \u0627\u0644\u0642\u0644\u0628\u064a \u0627\u0644\u062a\u0646\u0641\u0633\u064a.<\/li>\n<\/ul>\n

          \u00a0<\/strong><\/p>\n

          \u062e\u0637\u0637 \u0627\u0644\u0637\u0648\u0627\u0631\u0626<\/strong>\u00a0<\/strong><\/span><\/h1>\n

          \u0645\u0627 \u062a\u062d\u062a\u0627\u062c \u0625\u0644\u0649 \u0645\u0639\u0631\u0641\u062a\u0647<\/strong><\/span><\/h1>\n
            \n
          • \u064a\u062c\u0628 \u0623\u0646 \u062a\u0643\u0648\u0646 \u0647\u0646\u0627\u0643 \u062e\u0637\u0629 \u0644\u0644\u0627\u062e\u0644\u0627\u0621 \u0641\u064a \u0627\u0644\u0645\u062f\u0631\u0633\u0629 \u0648 \u0628\u0637\u0631\u064a\u0642\u0629 \u0639\u0645\u0644\u064a\u0629 \u0644\u0644\u0623\u0637\u0641\u0627\u0644 \u0627\u0644\u0630\u064a\u0646 \u064a\u0639\u0627\u0646\u0648\u0646 \u0645\u0646 \u0645\u062d\u062f\u0648\u062f\u064a\u0629 \u0623\u0648 \u0635\u0639\u0648\u0628\u0627\u062a \u062d\u0631\u0643\u064a\u0629 .<\/li>\n
          • \u0645\u0646 \u0627\u0644\u0645\u0647\u0645 \u0627\u0644\u0627\u0646\u062a\u0628\u0627\u0647 \u0648 \ufe97\ufea0\ufee8\ufe90 \u0627\ufedf\ufee4\ufeee\u0627\ufed7\ufed2 \u0627\ufedf\ufe98\ufef2 \ufed7\ufeaa \ufef3\u064f\u062f\u0647\u064e\u0633 \ufed3\ufef4\ufeec\ufe8e \u0627\ufef7\ufed3\ufeae\u0627\u062f ( \u0645\u062b\u0644 \u062d\u0627\u0644\u0627\u062a \u0627\u0644\u0632\u062d\u0627\u0645 )<\/li>\n
          • \u064a\u062c\u0628 \u0623\u0646 \u064a\u0643\u0648\u0646 \u0627\u0644\u0637\u0641\u0644 \u0642\u0627\u062f\u0631\u064b\u0627 \u0639\u0644\u0649 \u0627\u0644\u0648\u0635\u0648\u0644 \u0625\u0644\u0649 \u0645\u0642\u0627\u0628\u0636 \u0627\u0644\u0623\u0628\u0648\u0627\u0628.<\/li>\n
          • \u0642\u062f \u064a\u062d\u062a\u0627\u062c \u0644\u062a\u062d\u062f\u064a\u062f \u0634\u062e\u0635 \u0645\u0633\u0627\u0639\u062f \u0627\u0636\u0627\u0641\u064a \u0648 \u0627\u062d\u062a\u064a\u0627\u0637\u064a \u0625\u0630\u0627 \u0643\u0627\u0646 \u0647\u0630\u0627 \u0627\u0644\u0634\u062e\u0635 \u0627\u0644\u0645\u062a\u0627\u0628\u0639 \u0644\u0644\u0637\u0641\u0644 \u0644\u064a\u0633 \u0645\u062a\u0648\u0627\u062c\u062f \u0623\u0648 \u0645\u0634\u063a\u0648\u0644 .<\/li>\n
          • \u064a\u062c\u0628 \u0623\u0646 \u062a\u0643\u0648\u0646 \u062e\u0637\u0629 \u0639\u0644\u0627\u062c \u0627\u0644\u0635\u0631\u0639 \u0648\u0627\u0636\u062d\u0629 \u0648 \u0645\u0639\u0631\u0648\u0641\u0647 \u0644\u062f\u0649 \u0627\u0644\u0645\u062f\u0631\u0633\u064a\u0646 .<\/li>\n
          • \u0641\u064a \u062d\u0627\u0644 \u0627\u0644\u062d\u0627\u062c\u0629 \u0644\u0627\u062c\u0647\u0632\u0629 \u0627\u0644\u0627\u0646\u0639\u0627\u0634 \u0627\u0644\u0642\u0644\u0628\u064a \u0643\u0630\u0644\u0643 \u064a\u062d\u062a\u0627\u062c \u062a\u062f\u0631\u064a\u0628 \u0627\u0644\u0645\u062f\u0631\u0633\u064a\u0646 \u0639\u0644\u064a\u0647\u0627 .<\/li>\n<\/ul>\n

            \u0645\u0627 \u062a\u0633\u062a\u0637\u064a\u0639 \u0641\u0639\u0644\u0647<\/span><\/h1>\n
              \n
            • \u0648\u0636\u0639 \u062e\u0637\u0629 \u0644\u0644\u0637\u0648\u0627\u0631\u0626 \u0625\u0630\u0627 \u0644\u0632\u0645 \u0627\u0644\u0623\u0645\u0631 \u060c \u062a\u0639\u062a\u0645\u062f \u0639\u0644\u0649 \u0627\u062d\u062a\u064a\u0627\u062c\u0627\u062a \u0627\u0644\u0637\u0641\u0644 \u0627\u0644\u0641\u0631\u062f\u064a\u0629.<\/li>\n
            • \u062a\u0639\u064a\u064a\u0646 \u0627\u0634\u062e\u0627\u0635 \u0627\u062d\u062a\u064a\u0627\u0637\u064a\u064a\u0646 \u0639\u0646\u062f \u0627\u0644\u062d\u0627\u062c\u0629.<\/strong><\/li>\n<\/ul>\n

              \u0627\u0644\u0645\u0631\u0627\u062c\u0639<\/span><\/h1>\n

              \u0645\u0648\u0642\u0639 \u0627\u0644\u0648\u0631\u0627\u062b\u0629 \u0627\u0644\u0637\u0628\u064a\u0629<\/strong><\/p>\n

              \u0645\u0648\u0642\u0639 \u062c \u0623\u064a \u0623\u0645 \u0627\u0633 \u0623\u0633 (<\/strong>gemss<\/strong> )\u0644\u0644\u0645\u0648\u0627\u062f \u0627\u0644\u062a\u0639\u0644\u064a\u0645\u064a\u0629 \u0627\u0644\u0648\u0631\u0627\u062b\u064a\u0629 \u0644\u0644\u0645\u062f\u0627\u0631\u0633<\/strong><\/p>\n

              \u0645\u0648\u0627\u0642\u0639 \u0637\u0628\u064a\u0629 \u0645\u062a\u0639\u062f\u062f\u0629<\/strong><\/p>\n

              \u00a0<\/strong><\/p>\n

              \u062a\u0623\u0644\u064a\u0641<\/span><\/h1>\n

              \u0627\u0639\u062f\u0647\u0627 \u0644\u0644\u0646\u062a<\/strong>\u00a0\u062f. \u0639\u0628\u062f\u0627\u0644\u0631\u062d\u0645\u0646 \u0627\u0644\u0633\u0648\u064a\u062f<\/strong><\/p>\n","protected":false},"excerpt":{"rendered":"

              \u0623\u0645\u0631\u0627\u0636 \u0639\u062f\u064a\u062f\u0627\u062a \u0627\u0644\u0633\u0643\u0631\u064a\u0627\u062a \u0627\u0644\u0645\u062e\u0627\u0637\u064a\u0629 mucopolysaccharidosis \u0645\u0639\u0644\u0648\u0645\u0627\u062a \u0637\u0628\u064a\u0629 \u0647\u064a \u0623\u0645\u0631\u0627\u0636 \u0648\u0631\u0627\u062b\u064a\u0629 \u0646\u0627\u062c\u0645\u0629 \u0639\u0646 \u062e\u0644\u0644 \u0641\u064a \u0645\u0627 \u064a\u0633\u0645\u0649 \u0627\u0644\u0644\u064a\u0633\u0648\u0633\u0648\u0645 (lysosome) \u0648\u0647\u0648 \u0627\u0644\u062c\u0632\u0621 \u0627\u0644\u0645\u0633\u0626\u0648\u0644 \u0639\u0646 \u0627\u0644\u0645\u0648\u0627\u062f \u063a\u064a\u0631 \u0627\u0644\u0645\u0631\u063a\u0648\u0628 \u0641\u064a\u0647\u0627 \u062f\u0627\u062e\u0644 \u0627\u0644\u062e\u0644\u0627\u064a\u0627. \u0648\u062a\u0635\u0646\u0641 \u0627\u064a\u0636\u0627 \u0645\u0646 \u0623\u0645\u0631\u0627\u0636 \u0627\u0644\u062a\u062e\u0632\u064a\u0646 ( Storage Disease)\u00a0 \u0644\u0623\u0646 \u0627\u0644\u062c\u0633\u0645 \u064a\u0638\u0644 \u0639\u0627\u062c\u0632\u0627 \u0639\u0646 \u062a\u0646\u0638\u064a\u0641 \u0648\u062d\u0631\u0642 \u0648\u062a\u0643\u0633\u064a\u0631 \u062a\u0644\u0643 \u0627\u0644\u0645\u0648\u0627\u062f \u0641\u062a\u062a\u0631\u0627\u0643\u0645 \u0628\u062f\u0627\u062e\u0644 \u0627\u0644\u062e\u0644\u064a\u0629 \u0648 \u0627\u0644\u0627\u0646\u0633\u062c\u0629 \u0641\u062a\u0633\u0628\u0628 \u062e\u0644\u0644 \u0641\u064a \u0648\u0638\u0627\u0626\u0641\u0647\u0627. …<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[75],"tags":[],"class_list":["post-11985","post","type-post","status-publish","format-standard","hentry","category-mucopolysaccharidosis"],"_links":{"self":[{"href":"https:\/\/www.werathah.com\/special\/wp-json\/wp\/v2\/posts\/11985","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.werathah.com\/special\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.werathah.com\/special\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.werathah.com\/special\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/www.werathah.com\/special\/wp-json\/wp\/v2\/comments?post=11985"}],"version-history":[{"count":5,"href":"https:\/\/www.werathah.com\/special\/wp-json\/wp\/v2\/posts\/11985\/revisions"}],"predecessor-version":[{"id":12029,"href":"https:\/\/www.werathah.com\/special\/wp-json\/wp\/v2\/posts\/11985\/revisions\/12029"}],"wp:attachment":[{"href":"https:\/\/www.werathah.com\/special\/wp-json\/wp\/v2\/media?parent=11985"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.werathah.com\/special\/wp-json\/wp\/v2\/categories?post=11985"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.werathah.com\/special\/wp-json\/wp\/v2\/tags?post=11985"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}